Article ID | Journal | Published Year | Pages | File Type |
---|---|---|---|---|
9243514 | Gastroentérologie Clinique et Biologique | 2005 | 4 Pages |
Abstract
Langerhans' cell histiocytosis is a disorder in children or young adults, characterized by clonal proliferation of histiocytic cells, staining for CD1a, with uni or multifocal organ involvement. It's a rare condition in adults. We report a case of Langerhans' cell histiocytosis in an adult with sclerosing cholangitis which rapidly progressed to fatal liver failure and progressive cerebellar atrophy. Langerhans cell histiocytosis is a rare cause of sclerosing cholangititis in adults.
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Authors
Jérôme Desrame, Dominique BÃchade, Gilles Defuentes, Pascal Goasdoue, Jean-Jacques Raynaud, Valère Claude, Jean-Luc Renard, Thierry Genereau, Gilles Coutant, Jean-Pierre Algayres,