کد مقاله | کد نشریه | سال انتشار | مقاله انگلیسی | نسخه تمام متن |
---|---|---|---|---|
4161034 | 1607120 | 2016 | 5 صفحه PDF | دانلود رایگان |
• Surgery in adult HD is difficult because of chronic fibrous changes of the rectum.
• Surgeons should decide on the operative procedure and staged surgery.
• Staged operations including the Duhamel-GIA method are a viable surgical option.
Adult Hirschsprung's disease is a rare motor disorder of the gut that is frequently misdiagnosed as refractory constipation. We describe a 30-year-old patient with adult Hirschsprung's disease with a history of chronic constipation requiring daily enema. Barium enema and rectal biopsy showed short segment-type Hirschsprung's disease with a grossly distended sigmoid colon with fecal retention. Staged operations, including the Duhamel-GIA method as a definitive surgery, completely resolved the patient's symptoms. There were no complications by the end of a 7-year follow-up. Adult Hirschsprung's disease should be considered in the differential diagnosis of cases where adult patients present with chronic constipation. Despite technical difficulty of the modified Duhamel-GIA procedure due to chronic fibrous changes of the rectum, it is a feasible surgical option for treating cases of adult Hirschsprung's disease.
Journal: Journal of Pediatric Surgery Case Reports - Volume 13, October 2016, Pages 1–5