Sarcoma fibromixoide de bajo grado intracraneal: a propósito de un caso

The aim of this report is to show the MRI and CT findings for an extra-axial intracranial low-grade fibromyxoid sarcoma. To our knowledge, only three similar cases have been reported to date. We present the case of an 18-year-old woman who presented with a five-month history of hypoacusia, tinnitus, occipital headache, and left facial paresis. CT showed a large, homogeneous, expansive lesion in the left pontocerebellar angle that was eroding the promontory and affecting the posterior jugular foramen. At MRI, the lesion was homogeneous and isointense with respect to the cerebral parenchyma on T1-weighted sequences and heterogeneous and hypointense on T2-weighted sequences; after the administration of contrast material, it showed intense, homogeneous enhancement. The definitive diagnosis was established by histopathologic and immunohistochemical study.