Primitive neuroectodermal tumor of kidney mimicking as an inflammatory renal mass

Renal PNET should be kept in the differentials of a renal SOL presenting in adolescents and young adults. All diagnostic modalities concerning SOL of the kidney must be interpreted with caution in order for the appropriate management. Punctures for cytology can be indicated in select cases. Histopathology, immuno histochemistry supported by cytogenetic studies are required for the exact diagnosis of renal PNET. Multidisciplinary approach consisting of surgery, chemotherapy, and radiotherapy is recommended to manage this condition in view of its aggressive nature and poor prognosis.