دانلود مقالات ISI درباره اسید 3-هیدروکسی گلوتاریک + ترجمه فارسی

Immunolocalization of glutaryl-CoA dehydrogenase (GCDH) in adult and embryonic rat brain and peripheral tissues

Keywords: اسید 3-هیدروکسی گلوتاریک; 1H-MRS; proton magnetic resonance spectroscopy; 3-OHGA; 3-hydroxyglutaric acid; BBB; blood brain barrier; BSA; bovine serum albumin; CNS; central nervous system; DEPC; diethyl-pyrocarbonate; GA; glutaric acid; GA-I; glutaric aciduria type I; GalC; galacto

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2017 سفارش ترجمه

Acute lysine overload provokes protein oxidative damage and reduction of antioxidant defenses in the brain of infant glutaryl-CoA dehydrogenase deficient mice: A role for oxidative stress in GA I neuropathology

Keywords: اسید 3-هیدروکسی گلوتاریک; Glutaric acidemia type I; Brain damage; Antioxidant defenses; Glutaric acid; 3-Hydroxyglutaric acid; Infant Gcdh−/− mice

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2014 سفارش ترجمه

Marked reduction of Na+, K+-ATPase and creatine kinase activities induced by acute lysine administration in glutaryl-CoA dehydrogenase deficient mice

Keywords: اسید 3-هیدروکسی گلوتاریک; CK; creatine kinase; DCIP; dichloroindophenol; EDTA; ethylenediaminetetracetic acid; GA; glutaric acid; GA I; glutaric acidemia type I; GCDH; glutaryl-CoA dehydrogenase; Gcdh−/−; glutaryl-CoA dehydrogenase deficient mice; 3HGA; 3-hydroxyglutaric acid;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2012 سفارش ترجمه

Reduction of Na+, K+-ATPase activity and expression in cerebral cortex of glutaryl-CoA dehydrogenase deficient mice: A possible mechanism for brain injury in glutaric aciduria type I

Keywords: اسید 3-هیدروکسی گلوتاریک; CK; creatine kinase; DCIP; dichloroindophenol; DNP; dinitrophenol; EDTA; ethylenediaminetetracetic acid; EGTA; ethylene glycol-bis(2-aminoethylether)-N,N,N′,N′-tetraacetic acid; GA; glutaric acid; GA I; glutaric acidemia type I; GCDH; glutaryl-CoA deh

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2012 سفارش ترجمه

Complementary dietary treatment using lysine-free, arginine-fortified amino acid supplements in glutaric aciduria type I - A decade of experience

Keywords: اسید 3-هیدروکسی گلوتاریک; 3-OH-GA; 3-hydroxyglutaric acid; AAS; amino acid supplement; ANOVA; analysis of variance; BBB; blood-brain barrier; CAT1; cationic amino acid transporter 1; GA; glutaric acid; GA-I; glutaric aciduria type I; GCDH; glutaryl-CoA dehydrogenase (EC 1.3.99.7

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2012 سفارش ترجمه

The unsolved puzzle of neuropathogenesis in glutaric aciduria type I

Keywords: اسید 3-هیدروکسی گلوتاریک; 3-OHGA; 3-hydroxyglutaric acid; AMPA; α-amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid; APV; D-2-amino-5-phophonovalerate; BBB; blood-brain barrier; BCB; blood-cerebrospinal fluid barrier; CAT; catalase; CHO; Chinese hamster ovary; CK; creatine k

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2011 سفارش ترجمه

Glutaric aciduria type 1: Clinical, biochemical and molecular findings in patients from Israel

Keywords: اسید 3-هیدروکسی گلوتاریک; GCDH mutations; Prenatal diagnosis; Acylcarnitines; Glutarylcarnitine; Glutaric acid; 3-hydroxyglutaric acid

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2007 سفارش ترجمه

Stable-isotope dilution gas chromatography-mass spectrometric measurement of 3-hydroxyglutaric acid, glutaric acid and related metabolites in body fluids of patients with glutaric aciduria type 1 found in newborn screening

Keywords: اسید 3-هیدروکسی گلوتاریک; Glutaric acid; 3-Hydroxyglutaric acid; Newborn screening; Carnitine;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2005 سفارش ترجمه

Novel metabolic and molecular findings in hepatic carnitine palmitoyltransferase I deficiency

Keywords: اسید 3-هیدروکسی گلوتاریک; Carnitine palmitoyltransferase I deficiency; CPT1A gene mutation; Mitochondrial fatty acid oxidation; Urine organic acids; Dicarboxylic aciduria; 3-Hydroxyglutaric acid; Glutaric acid; Dodecanedioic; Tandem MS; Acylcarnitines;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2005 سفارش ترجمه

Quantification of glutaric and 3-hydroxyglutaric acids in urine of glutaric acidemia type I patients by HPLC with intramolecular excimer-forming fluorescence derivatization

Keywords: اسید 3-هیدروکسی گلوتاریک; Glutaric aciduria; 3-Hydroxyglutaric acid; Glutaric acid; Excimer-forming fluorescence;

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2005 سفارش ترجمه