دانلود مقالات ISI درباره Abca3 + ترجمه فارسی

مقالات اصلی اهدای پیوند ریه برای نوزادان و کودکان مبتلا به اختلالات ژنتیکی متابولیسم سورفکتانت

Original ArticlesOutcomes of Lung Transplantation for Infants and Children with Genetic Disorders of Surfactant Metabolism

Keywords: surfactant protein B; surfactant protein C; ABCA3; SFTPB; SFTPC; NKX2.1; childhood interstitial lung disease; neonatal respiratory distress syndrome; chILD; RDS; pediatric lung transplantation; ABCA3; Adenosine triphosphate-binding cassette member A3; c

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2017 سفارش ترجمه

به روز رسانی در مورد بیماری های ریوی در کودکان

Update on Diffuse Lung Disease in Children

Keywords: interstitial lung disease; pediatric pulmonology; recent advances in chest medicine; ABCA3; gene encoding adenosine 5′-triphosphate-binding cassette family member A-3; ANCA; antineutrophil cytoplasmic antibody; ATS; American Thoracic Society; COPA; coat

دانلود رایگان متن کامل مقاله ISI 29 صفحه سال انتشار : 2016 سفارش ترجمه

اثر هیپوکسیا بر بیان ژن ریه و پروتئومیک مشخصات: بینش واکنش سورفاکتانت ریوی

Effect of hypoxia on lung gene expression and proteomic profile: Insights into the pulmonary surfactant response

Keywords: Lung surfactant; Surfactant proteins; Hemoglobin; Air–liquid interface; ABCA3

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2014 سفارش ترجمه

TGF beta inhibits expression of SP-A, SP-B, SP-C, but not SP-D in human alveolar type II cells

Keywords: ABCA3; Surfactant proteins; Pulmonary fibrosis; Lung;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2018 سفارش ترجمه

Aberrant lung remodeling in a mouse model of surfactant dysregulation induced by modulation of the Abca3 gene

Keywords: PL; phospholipid; ABCA; ATP binding cassette class A; SP-C; surfactant protein C; SFTPC; gene encoding SP-C proprotein; DPLD; diffuse parenchymal lung disease; LB; lamellar body; BAL; bronchoalveolar lavage; Pulmonary; Surfactant; Phospholipids; ABCA3; Lu

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2017 سفارش ترجمه

Quantification of volume and lipid filling of intracellular vesicles carrying the ABCA3 transporter

Keywords: ABCA3; Interstitial lung disease (ILD); Respiratory distress syndrome; Surfactant; Functional analysis; K1388N; E292V;

دانلود رایگان متن کامل مقاله ISI 30 صفحه سال انتشار : 2017 سفارش ترجمه

Spectral phasor analysis of LAURDAN fluorescence in live A549 lung cells to study the hydration and time evolution of intracellular lamellar body-like structures

Keywords: LAURDAN; 6-dodecanoyl-2-dimethylaminonaphthalene; LBs; lamellar bodies; GP; generalized polarization function; FWHM; full width of the half maximum, MVB, multivesicular bodies; PS; pulmonary surfactant; ABCA3; ATP-binding cassette transporter A3; LAURDAN;

دانلود رایگان متن کامل مقاله ISI 28 صفحه سال انتشار : 2016 سفارش ترجمه

ABCA3 protects alveolar epithelial cells against free cholesterol induced cell death

Keywords: Diffuse parenchymal lung disease; ABC transporter; ABCA3; Pulmonary surfactant; Cholesterol;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2015 سفارش ترجمه

Novel ABCA3 mutations as a cause of respiratory distress in a term newborn

Keywords: RDS; respiratory distress syndrome; LB; lamellar bodies; SFTPB; surfactant protein-B; SFTPC; surfactant protein-C; NKX2-1; thyroid transcription factor-1; ABCA3; ATP-binding cassette A3 transporter; CT; computed tomography; BAL; broncho-alveolar lavage; D

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2014 سفارش ترجمه

Synonymous ABCA3 Variants Do Not Increase Risk for Neonatal Respiratory Distress Syndrome

Keywords: ABCA3; Adenosine triphosphate-binding cassette A3 transporter; ESP; Exome Sequencing Project; MAF; Minor allele frequency; RDS; Respiratory distress syndrome;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2014 سفارش ترجمه

A rapid method to assess the stage differentiation in Leishmania donovani by flow cytometry

Keywords: FCM; Flow cytometry; FSC; Forward scatter; SSC; Side scatter; Promastigote; LdAxAm; Leishmania donovani axenic amastigote; Amastin gene; ABCA3; ATP binding cassette A3; SAcP; Secretory acid phosphatase; 3′-Nucleotidase.;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2012 سفارش ترجمه

Analysis of gene expression profiles in alveolar epithelial type II-like cells differentiated from human alveolar epithelial progenitor cells

Keywords: ABCA3; ATP-binding cassette, sub-family A (ABC1), member 3; AEPC; alveolar epithelial progenitor cell; ATI; alveolar epithelial type I; ATII; alveolar epithelial type II; CDH1; cadherin 1, type 1; C/EBP; CCAAT/enhancer-binding protein; CEBPD; CCAAT/enhanc

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2012 سفارش ترجمه

Surfactant Dysfunction

Keywords: Newborn; Respiratory Distress Syndrome; Genetic Basis of Disease; Interstitial Lung Disease; Pulmonary Fibrosis; ABCA3; NKX2.1

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

New Entities and Diagnostic Challenges in Pediatric Lung Disease

Keywords: Pediatric; Lung; Alveolar capillary dysplasia; Genetic surfactant disorders; ABCA3; TTF1; Pulmonary interstitial glycogenosis; Neuroendocrine cell hyperplasia of infancy;

دانلود رایگان متن کامل مقاله ISI 19 صفحه سال انتشار : 2010 سفارش ترجمه

Inherited Surfactant Deficiency Caused by Uniparental Disomy of Rare Mutations in the Surfactant Protein-B and ATP Binding Cassette, Subfamily A, Member 3 Genes

Keywords: ABCA3; ATP binding cassette subfamily A, member 3; ABCA3; ABCA3 gene; PCR; Polymerase chain reaction; SP-B; Surfactant protein-B; SFTPB; SP-B gene; SP-C; Surfactant protein-C; SFTPC; SP-C gene; UPD; Uniparental disomy;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2009 سفارش ترجمه

Usual Interstitial Pneumonia in an Adolescent With ABCA3 Mutations*

Keywords: ABCA3; children; interstitial lung disease; surfactant; usual interstitial pneumoniaABCA3, adenosine triphosphate-binding-cassette-A3 gene; IPF, idiopathic pulmonary fibrosis; ILD, interstitial lung disease; SFTPC, surfactant protein C gene; UIP, usual in

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2008 سفارش ترجمه

Pathologies respiratoires associées à des anomalies héréditaires du métabolisme du surfactant

Keywords: Surfactant; Détresse respiratoire; Protéine B du surfactant; Protéine C du surfactant; ABCA3; TTF-1

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2008 سفارش ترجمه

Targeted inactivation of the murine Abca3 gene leads to respiratory failure in newborns with defective lamellar bodies

Keywords: ABCA3; Transgenic mouse model; Lamellar body; Respiratory distress syndrome; Surfactant; Newborn; Atelectasis

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2007 سفارش ترجمه

Unexplained Neonatal Respiratory Distress Due to Congenital Surfactant Deficiency

Keywords: ABCA3; Adenosine triphosphate-binding cassette protein, member A3; PAS; Periodic acid-Schiff reagent; PCR; Polymerase chain reaction; SP-B; Surfactant protein B; SP-C; Surfactant protein C;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2007 سفارش ترجمه

The genetics of neonatal respiratory disease

Keywords: Respiratory distress syndrome (RDS); Bronchopulmonary dysplasia; Surfactant proteins; SP-A; SP-B; SP-C; SP-D; ABCA3; Alveolar proteinosis; Transient tachypnoea of the newborn (TTN); Cystic fibrosis (CF) screening; Primary ciliary dyskinesia (PCD);

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2005 سفارش ترجمه