Keywords: Heterotopic ossification; Fibrodysplasia Ossificans Progressiva; Chondrogenesis and osteogenesis; Retinoid signaling; Retinoid nuclear receptors; ALK2; BMP signaling; Hereditary Multiple Exostoses; Multiple Osteochondromas;
مقالات ISI (ترجمه نشده)
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Keywords: ALKs; activin receptor-like (type I) kinases; BMP; bone morphogenetic protein; BMPRII; BMP type II receptor; FKBP12; FK506-binding protein 12â¯kDa; FOP; Fibrodysplasia Ossificans Progressiva; AMPK; AMP-activated protein kinase; SMKI; small molecule kinas
Keywords: ACVR; activin A receptor; ALK; activin receptor-like kinase; BMP; bone morphogenetic protein; BOP; blast over pressure; COX; cyclo-oxygenase; CT; computed tomography; ECM; extracellular matrix; FOP; fibrodysplasia ossificans progressiva; HES; hydroxy-ethy
Prevalence and risk factors for kidney stones in fibrodysplasia ossificans progressiva
Keywords: Fibrodysplasia ossificans progressiva; Nephrolithiasis; Kidney stones;
Longitudinal patient-reported mobility assessment in fibrodysplasia ossificans progressiva (FOP)
Keywords: Fibrodysplasia ossificans progressiva; Heterotopic ossification; ACVR1; Joint function; Patient-reported outcomes;
Fibrodysplasia ossificans progressiva in China
Keywords: Fibrodysplasia ossificans progressiva; Epidemiology; Research; Diagnosis; China;
Structural basis for the potent and selective binding of LDN-212854 to the BMP receptor kinase ALK2
Keywords: BMP; Heterotopic ossification; Kinase inhibitor; Crystal structure; Drug; Fibrodysplasia ossificans progressiva;
Fibrodysplasia ossificans progressiva: The patient voice
Keywords: Fibrodysplasia ossificans progressiva;
The FOP Connection Registry: Design of an international patient-sponsored registry for Fibrodysplasia Ossificans Progressiva
Keywords: Fibrodysplasia Ossificans Progressiva; International FOP Association; Registry; Heterotopic ossification; Natural history; Patient-reported;
Is heterotopic ossification getting nervous?: The role of the peripheral nervous system in heterotopic ossification
Keywords: HO; heterotopic ossification; BMP; bone morphogenetic protein; BNB; blood-nerve barrier; TRPV1; transient receptor potential cation channel subfamily V member 1; sP; substance P; CGRP; Calcitonin gene-related protein; DRG; dorsal root ganglion; BBB; blood
The obligatory role of Activin A in the formation of heterotopic bone in Fibrodysplasia Ossificans Progressiva
Keywords: Fibrodysplasia Ossificans Progressiva; Heterotopic Ossification; Activin A; ACVR1; Anti-Activin antibody; Progenitor cells;
Imaging assessment of fibrodysplasia ossificans progressiva: Qualitative, quantitative and questionable
Keywords: FOP; fibrodysplasia ossificans progressiva; CT; computed tomography; HO; heterotopic bone; ACVR1; activin A type I receptor; ALK2; activin-like kinase2; mSv; millisievert; AP; anterioposterior; MRI; magnetic resonance imaging; US; Ultrasonography; 99Â m T
Application of human induced pluripotent stem cells to model fibrodysplasia ossificans progressiva
Keywords: Human induced pluripotent stem cells; Fibrodysplasia ossificans progressiva; Activin A type I receptor; Human disease models;
Clinical-pathological correlations in three patients with fibrodysplasia ossificans progressiva
Keywords: Fibrodysplasia ossificans progressiva; Heterotopic ossification; Thoracic insufficiency syndrome; Restrictive lung disease; Cardiomyopathy; Autopsy;
Periodontal ligament fibroblasts as a cell model to study osteogenesis and osteoclastogenesis in fibrodysplasia ossificans progressiva
Keywords: Fibrodysplasia ossificans progressiva; Periodontal ligament fibroblasts; Osteogenesis; Osteoclastogenesis; TGF-β/BMP superfamily;
Drosophila models of FOP provide mechanistic insight
Keywords: Fibrodysplasia Ossificans Progressiva; ACVR1; ALK2; Sax; BMP signaling; Heterotopic ossification;
Variable signaling activity by FOP ACVR1 mutations
Keywords: ACVR1; activin A receptor type 1; BMP; bone morphogenetic protein; HO; heterotopic ossification; FOP; fibrodysplasia ossificans progressiva; LBD; extracellular ligand-binding domain; GS; glycine-serine rich domain; PK; protein kinase domain; TGF-beta; tra
Stem cells and heterotopic ossification: Lessons from animal models
Keywords: Animal models; Heterotopic ossification; Stem cells; Progenitor cells; Fibrodysplasia ossificans progressiva; FOP; ACVR1; ALK2; Activin; BMP; Fibro/adipogenic progenitors; FAPs; Satellite cell; Endothelium; Skeletal muscle; Tendon; PDGFRα; TIE2; Scleraxi
Joint-specific risk of impaired function in fibrodysplasia ossificans progressiva (FOP)
Keywords: Fibrodysplasia ossificans progressiva; Heterotopic ossification; Bone morphogenetic protein signaling; ACVR1; Joint survival; Risk;
Molecular mechanisms for activation of mutant activin receptor-like kinase 2 in fibrodysplasia ossificans progressiva
Keywords: Fibrodysplasia ossificans progressiva; BMP; ALK2; Receptors;
Analog Method for Radiographic Assessment of Heterotopic Bone in Fibrodysplasia Ossificans Progressiva
Keywords: Heterotopic bone; fibrodysplasia ossificans progressiva;
The congenital great toe malformation of fibrodysplasia ossificans progressiva? - A close call
Keywords: Fibrodysplasia ossificans progressiva; Heterotopic ossification; Brachydactyly; Bone morphogenetic protein (BMP) signaling; ACVR1; BMP receptor IB;
AMPK downregulates ALK2 via increasing the interaction between Smurf1 and Smad6, leading to inhibition of osteogenic differentiation
Keywords: Fibrodysplasia ossificans progressiva; Activin A receptor type I/activin receptor like kinase 2; AMP-activated protein kinase; Osteogenic differentiation; iPS;
A cumulative analogue joint involvement scale (CAJIS) for fibrodysplasia ossificans progressiva (FOP)
Keywords: Fibrodysplasia ossificans progressiva; Heterotopic ossification; Bone morphogenetic protein signaling; ACVR1; Activities of daily living; Ambulation;
Fibrodysplasia ossificans progressiva. A case report and focus on the BMP signaling pathway
Keywords: Fibrodysplasia ossificans progressiva; BMP; Ossification; Pathophysiology; Dysplasie ossifiante progressive; BMP; Ossification; Physiopathologie;
A novel ACVR1 mutation detected by whole exome sequencing in a family with an unusual skeletal dysplasia
Keywords: Whole exome sequencing; ACVR1; Skeletal dysplasia; Fibrodysplasia ossificans progressiva; FOP variant
ACVR1-Fc suppresses BMP signaling and chondro-osseous differentiation in an in vitro model of Fibrodysplasia ossificans progressiva
Keywords: Fibrodysplasia ossificans progressiva; Heterotopic ossification; BMP signaling; ACVR1; ALK2;
Osteogenic potential of alpha smooth muscle actin expressing muscle resident progenitor cells
Keywords: αSMA; alpha smooth muscle actin; BMP; bone morphogenetic protein; FOP; fibrodysplasia ossificans progressiva; HO; heterotopic ossification; MyHC; myosin heavy chain; Heterotopic ossification; Mesenchymal progenitor; Alpha smooth muscle actin; Satellite c
Common mutations in ALK2/ACVR1, a multi-faceted receptor, have roles in distinct pediatric musculoskeletal and neural orphan disorders
Keywords: ACVR1; ALK2; Fibrodysplasia Ossificans Progressiva; Diffuse Intrinsic Pontine Gliomas; Orphan diseases; BMP signaling
Original Full Length ArticleInhibition of TGFβ signaling decreases osteogenic differentiation of fibrodysplasia ossificans progressiva fibroblasts in a novel in vitro model of the disease
Keywords: FOP; fibrodysplasia ossificans progressiva; FCS; fetal calf serum; BMP; bone morphogenetic protein; TGFβ; transforming growth factor β; Runx2; runt-related transcription factor 2; Alp; alkaline phosphatase; OC; osteocalcin; ACVR1; activin receptor IA; A
Muscle imaging in fibrodysplasia ossificans progressiva: The neurologist's perspective
Keywords: Fibrodysplasia ossificans progressiva; FOP; Muscle MRI; Muscle imaging;
Establishment of a novel model of chondrogenesis using murine embryonic stem cells carrying fibrodysplasia ossificans progressiva-associated mutant ALK2
Keywords: Fibrodysplasia ossificans progressiva; BMP receptor; Embryonic stem cells; Chondrocytes;
The phenotype and genotype of fibrodysplasia ossificans progressiva in China: A report of 72 cases
Keywords: Fibrodysplasia ossificans progressiva; Heterotopic ossification; Bone morphogenetic protein; ACVR1; ALK2;
¿Hay lugar en atención primaria para las enfermedades poco frecuentes? El caso de la fibrodisplasia osificante progresiva
Keywords: Enfermedades raras; Fibrodisplasia osificante progresiva; Paradoja de la rarezaRare diseases; Fibrodysplasia ossificans progressiva; Paradox of rarity
Fungal pyrrolidine-containing metabolites inhibit alkaline phosphatase activity in bone morphogenetic protein-stimulated myoblastoma cells
Keywords: Lucilactaenes; Fungal metabolites; C2C12 myoblasts; Fibrodysplasia ossificans progressiva
Fibrodysplasia ossificans progressiva in Spain: epidemiological, clinical, and genetic aspects
Keywords: Fibrodysplasia ossificans progressiva; FOP; Heterotopic ossification; ACVR1; BMP type I receptor
Interaction of Tmem119 and the bone morphogenetic protein pathway in the commitment of myoblastic into osteoblastic cells
Keywords: Tmem119; Bone morphogenetic protein; Osteoblast; Myoblast; Fibrodysplasia ossificans progressiva; Muscle ossification;
Anterior-wall aneurysm of the internal carotid artery successfully treated solely by stenting: With special reference to etiology
Keywords: MRI; magnetic resonance imaging; FOP; fibrodysplasia ossificans progressiva; CT; computed tomography;
Loss-of-function of ACVR1 in osteoblasts increases bone mass and activates canonical Wnt signaling through suppression of Wnt inhibitors SOST and DKK1
Keywords: ACVR1; activin A receptor type I; ALK; activin receptor-like kinase; BMP; bone morphogenetic protein; BMPR; BMP receptor; DEXA; dual-emission X-ray absorptiometry; E; embryonic day; FOP; fibrodysplasia ossificans progressiva; HBM; high bone mass; P; postn
Scalp nodules as a presenting sign of fibrodysplasia ossificans progressiva: A register-based study
Keywords: fibrodysplasia ossificans progressiva; hallux valgus; heterotopic ossification; neonatal nodules; nodular fasciitis
A novel ACVR1 mutation in the glycine/serine-rich domain found in the most benign case of a fibrodysplasia ossificans progressiva variant reported to date
Keywords: Fibrodysplasia ossificans progressiva; FOP; ACVR1; Heterotopic ossification; Mutation
Dental Care for Patients Who Are Unable to Open Their Mouths
Keywords: Anesthesia; Fibrodysplasia ossificans progressiva; Mobius syndrome; Inanition; Awake fiberoptic intubation; Buccal access; Pemphigus; Rheumatoid arthritis
The FOP metamorphogene encodes a novel type I receptor that dysregulates BMP signaling
Keywords: Fibrodysplasia ossificans progressiva; Heterotopic ossification; Bone morphogenetic protein (BMP) receptor; BMP signaling; Metamorphosis; Metamorphogene; ACVR1; Activin-like kinase 2 (ALK2);
Applications of small molecule BMP inhibitors in physiology and disease
Keywords: High throughput screen; Bone morphogenetic protein; TGF-β; Anemia; Hepcidin; Cardiomyocyte; Embryonic stem cell; Fibrodysplasia ossificans progressiva; Bone mineral density