Keywords: جستجو; Angioedema without wheals; Nonhistaminergic angioedema; Hereditary angioedema; Idiopathic angioedema; Clinical characteristic; Angioedematous attack; C1-INH-HAE; Hereditary angioedema with C1-inhibitor deficiency; FXII-HAE; Hereditary angioedema with fact
مقالات ISI جستجو (ترجمه نشده)
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Keywords: جستجو; BHA; butylated hydroxyanisole; DPPH; 2,2-diphenyl-1-picrylhydrazyl; f; mass of CO2 per unit of initial dry material (kg CO2/kg dry bark); f0; parameter to take into account soaking of bark (kg CO2/kg initial dry bark); HAE; hydroalcoholic extract (dry bas
Keywords: جستجو; Angioedema; Bradykinin; ACE inhibitors; ARBs (angiotensin receptor blockers); Dipeptidyl peptidase IV inhibitors; Neprilysin inhibitors; Icatibant; ACEi; Angiotensin-converting-enzyme inhibitor; ANP; A-type natriuretic peptide; APP; Aminopeptidase P; ARB;
Keywords: جستجو; Hereditary angioedema; Icatibant; Home-based treatment; Bradykinin-receptor antagonist; AE; Adverse event; HAE; Hereditary angioedema; HCP-administration; Administration by health care professionals at medical facilities; ISR; Injection-site reaction; PSS
Keywords: جستجو; Hereditary angioedema; Bradykinin; C1 inhibitor deficiency; Bradykinin B2 receptor antagonist; Icatibant; Children; Adolescents; Pediatrics; Treatment; AE; adverse event; C1-INH; C1 inhibitor; C1-INH-HAE; hereditary angioedema with C1-inhibitor deficiency
Keywords: جستجو; Hereditary angioedema; Hereditary angioedema attacks; Treatment plan; Angioedema management; Emergency department; Angioedema guidelines; On-demand treatment; Patient-reported outcomes; Quality of life; Disease burden; ED; Emergency department; FDA; Food
Keywords: جستجو; HAE; hepatic arterial embolization;
Keywords: جستجو; Hereditary angioedema; angioedema attack; human C1-inhibitor; efficacy; complement system; contact system; BK; Bradykinin; B1R; Bradykinin receptor 1; B2R; Bradykinin receptor 2; C1INH; C1-inhibitor; CPM; Carboxypeptidase M; CPN; Carboxypeptidase N; FXI;
Keywords: جستجو; 2D-LC; two-dimensional liquid chromatography; AA; amino acid; AC; affinity chromatography; ADC; antibody-drug conjugates; ADCC; antibody-dependent cellular cytotoxicity; AF4; asymmetric flow field fractionation; APTS; 1-aminopyrene-3,6,8-trisulfonate; Asn
Keywords: جستجو; Pediatric hereditary angioedema; Hereditary angioedema; Age onset; C1-INH; C1 inhibitor; CCHMC; Cincinnati Children's Hospital Medical Center; EMR; Electronic medical records; ER; Emergency room; HAE; Hereditary angioedema; IQR; Interquartile range; pdC1I
Keywords: جستجو; DEB; drug-eluting bead; EHD; extrahepatic disease; HAE; hepatic artery embolization; HCC; hepatocellular carcinoma; HR; hazard ratio; LN; lymph node; OS; overall survival; PFS; progression-free survival; SHARP; Sorafenib HCC Assessment Randomized Protocol
Keywords: جستجو; Anaphylaxis; mast cell; bradykinin; mouse models; tryptase; contact system; ACE; Angiotensin-converting enzyme; Anti-Xa; Anti-factor Xa activity; aPTT; Activated partial thromboplastin time; Bdkrb1; B1R coding gene; Bdkrb2; B2R coding gene; B1R; Bradyki
Keywords: جستجو; CI; confidence interval; HAE; hepatic artery embolization; NET; neuroendocrine tumor; OS; overall survival;
Pegvaliase for the treatment of phenylketonuria: Results of a long-term phase 3 clinical trial program (PRISM)
Keywords: جستجو; ACMG; American College of Medical Genetics and Genomics; ADHD RS-IV IA; Attention Deficit Hyperactivity Disorder Rating Scale IV inattention subscale; AE; adverse event; CTCAE; Common Terminology Criteria for Adverse Events; DMC; Data Monitoring Committee
Health-Related Quality of Life with Subcutaneous C1-Inhibitor for Prevention of Attacks of Hereditary Angioedema
Keywords: جستجو; C1-inhibitor protein; Hereditary angioedema; Patient-reported outcomes; Quality of life; Productivity; Satisfaction; Subcutaneous; HAEGARDA; C1-INH; C1-inhibitor; C1-INH-HAE; Hereditary angioedema with C1-inhibitor deficiency; CI; Confidence interval; EQ-
Hereditary Angioedema with Normal C1 Inhibitor and F12 Mutations in 42 Brazilian Families
Keywords: جستجو; Hereditary angioedema; Normal C1 inhibitor; F12 mutations; Estrogen; Brazilian population; ACEI; Angiotensin-converting enzyme inhibitor; C1-INH; C1 inhibitor; C1-INH-HAE; Hereditary angioedema with C1 inhibitor deficiency; eOC; Estrogen-containing oral c
The Journal of Allergy and Clinical Immunology: In Practice 2017 Year in Review
Keywords: جستجو; Angioedema; Allergy; Asthma; Anaphylaxis; Atopic dermatitis; Contact dermatitis; Drug allergy; Eosinophilic esophagitis; Eosinophilia; Food allergy; Immunodeficiency; Immunotherapy; Rhinitis; Rhinosinusitis; Urticaria; AAAAI; American Academy of Allergy A
Pegvaliase for the treatment of phenylketonuria: A pivotal, double-blind randomized discontinuation Phase 3 clinical trial
Keywords: جستجو; ACMG; American College of Medical Genetics and Genomics; ADHD RS-IV IA; Attention Deficit Hyperactivity Disorder Rating Scale IV, inattention subscore; AE; adverse event; ANCOVA; analysis of covariance; CANTAB; Cambridge Neuropsychological Test Automated
Mutation of the angiopoietin-1 gene (ANGPT1) associates with a new type of hereditary angioedema
Keywords: جستجو; Hereditary angioedema; angiopoietin-1; gene; mutation; multimers; tunica interna endothelial cell kinase 2 receptor; ANGPT1; Angiopoietin-1; ANGPT2; Angiopoietin-2; C1-INH; C1 inhibitor; C1-INH-HAE; Hereditary angioedema caused by C1 inhibitor deficiency;
A review on the ethnomedicinal uses, phytochemistry and pharmacology of Alpinia officinarum Hance
Keywords: جستجو; ABS; Akaferd blood stopper; AN; Aspergillus niger; AO; Alpinia officinarum; BC; Bacillus cereus; B16-F10; Mouse melanoma cell line; CA; Candida albicans; CAR; Constitutive androstane receptor; CH2CL2; Dichloromethane; DPPH; Diphenylpicrylhydrazyl; EA; Eth
A novel prophylaxis with C1-inhibitor concentrate in hereditary angioedema during erythema marginatum
Keywords: جستجو; C1-inhibitor; C1-INH; C1-INH-HAE; hereditary angioedema with C1-inhibitor deficiency; EM; erythema marginatum; HAE; hereditary angioedema; mg; milligram; pdC1-INH; plasma-derived C1-inhibitor; C1-inhibitor deficiency; Erythema marginatum; Hereditary angio
Cytokine and estrogen stimulation of endothelial cells augments activation of the prekallikrein-high molecular weight kininogen complex: Implications for hereditary angioedema
Keywords: جستجو; Hereditary angioedema; C1 inhibitor; bradykinin; heat shock protein 90; APMSF; (4-Amidinophenyl)-methanesulfonyl fluoride; HAE; Hereditary angioedema; HK; High molecular weight kininogen; PAI-2; Plasminogen activator inhibitor-2; TPA; Tissue plasminogen a
Diminished capacity of opsonization and immune complex solubilization, and detection of anti-C1q antibodies in sera from patients with hereditary angioedema
Keywords: جستجو; Anti-C1q antibody; Autoimmune disease; Hereditary angioedema; Immune complex; Phagocytosis; C1-INH; C1 esterase inhibitor; CR; Complement receptor; HAE; Hereditary angioedema; IC; Immune complex; NHPS; Normal human pooled sera; PBS; Phosphate buffered sal
Recombinant Human C1-Esterase Inhibitor to Treat Acute Hereditary Angioedema Attacks in Adolescents
Keywords: جستجو; C1-esterase; Hereditary angioedema; Adolescent; Safety; Efficacy; Ruconest; Pharmacokinetics; AE; Adverse event; C1-INH; C1-esterase inhibitor; Cmax; Maximum concentration; HAE; Hereditary angioedema; IV; Intravenous; OLE; Open-label extension; RCT; Rando
Polysaccharide from Mesona chinensis: Extraction optimization, physicochemical characterizations and antioxidant activities
Keywords: جستجو; MCP; polysaccharide from Mesona chinensis; HAE; hot alkali extraction; DPPH; 1,1-diphenyl-2-picrylhydrazyl; FTIR; Fourier transform infrared spectroscopy; Mw; molecular weight; BBD; Box-Behnken design; RSM; response surface methodology; HPGPC; high perf
α-Pyrrolidinononanophenone provokes apoptosis of neuronal cells through alterations in antioxidant properties
Keywords: جستجو; AMC; 7-amido-4-methylcoumarin; AMPK; AMP kinase; BSO; DL-buthionine-(S,R)-sulfoximine; DCFH-DA; 6-carboxy-2â²,7â²-dichloro-dihydrofluorescein diacetate-di(acetoxymethylester); DEM; diethylmaleate; DMF; N,N-dimethylformamide; DPBS; Dulbecco's phosphate
Structural diversity of copper(II) amino alcoholate complexes
Keywords: جستجو; Hae; 2-aminoethanol; Hdmae; N,N-dimethylaminoethanol; Hdeae; N,N-diethylaminoethanol; Hap; 3-aminopropanol; Hdmap; N,N-dimethylaminopropanol; Hdeap; N,N-diethylaminopropanol; Hdpap; Hab, 4-aminobutanol; R-Hab; (R)-2-amino-butan-1-ol; Hape; 5-aminopentanol
The herbal medicine Melissa officinalis extract effects on gene expression of p53, Bcl-2, Her2, VEGF-A and hTERT in human lung, breast and prostate cancer cell lines
Keywords: جستجو; Her2; Human epidermal growth factor receptor 2; VEGF-A; Vascular endothelial growth factor-A; hTERT; Telomerase reverse transcriptase; MOE; Melissa officinalis extract; PPE; Pomegranate peel extract; PSE; Pomegranate seed extract; HAE; Hydroalcoholic extr
Optimization of the extraction process of polyphenols from Thymus serpyllum L. herb using maceration, heat- and ultrasound-assisted techniques
Keywords: جستجو; ANOVA; analysis of variance; CA; caffeic acid derivates; ChA; chlorogenic acid; CE; catechin equivalent; FC; Folin-Ciocalteu reagent; FL; flavonoids; GAE; gallic acid equivalent; HAE; heat-assisted extraction; HPLC; high performance liquid chromatography;
Peripheral Blood Regulatory T-Cell and Type 1 Helper T-Cell Population Decrease after Hepatic Artery Embolization
Keywords: جستجو; CD; cluster of differentiation; CTL; cytotoxic T lymphocytes; FOXP3; forkhead box P3; HAE; hepatic artery embolization; IFN-γ; interferon-γ; IL; interleukin-4; PBMC; peripheral blood mononuclear cell; Th1; type 1 helper T cells; Th2; type 2 helper T cel
C1-inhibitor efficiently delays clot development in normal human whole blood and inhibits Escherichia coli-induced coagulation measured by thromboelastometry
Keywords: جستجو; aPTT; activated partial thromboplastin time; C1-INH; C1-inhibitor; E. coli; Escherichia coli; EXTEM; extrinsic thromboelastometry; HAE; hereditary angioedema; HSA; human serum albumin; INTEM; intrinsic thromboelastometry; LI; lysis index; min; minute; NAT
Mechanisms of allergy and clinical immunologyDeficiency of plasminogen activator inhibitor 2 in plasma of patients with hereditary angioedema with normal C1 inhibitor levels
Keywords: جستجو; Hereditary angioedema; C1 inhibitor; bradykinin; plasminogen activator inhibitor; BCIP/NBT; 5-Bromo-4-chloroindolyl phosphate/nitroblue tetrazolium; C1-INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-N; Hereditary angioedema with normal C1 inhibitor le
Safety and Usage of C1-Inhibitor in Hereditary Angioedema: Berinert Registry Data
Keywords: جستجو; Berinert; Plasma-derived C1-INH; Patient registry; Thromboembolic event; Real-world; Prophylaxis; On demand; Self-administration; Safety; Dosing; AE; Adverse event; C1-INH; C1 inhibitor; DVT; Deep vein thrombosis; EU; European Union; HAE; Hereditary angio
Original ContributionsEfficacy of Different Medical Therapies for the Treatment of Acute Laryngeal Attacks of Hereditary Angioedema due to C1-esterase Inhibitor Deficiency
Keywords: جستجو; C1-INH; efficacy; HAE; laryngeal; re-dosing;
Tolerability and Effectiveness of 17-α-Alkylated Androgen Therapy for Hereditary Angioedema: A Re-examination
Keywords: جستجو; 17-α-Alkylated androgen; Hereditary angioedema; Treatment; Effectiveness; Side effects; C1 inhibitor; Severity; Danazol; Prophylaxis; AA; 17-α-Alkylated androgens; C1INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-nl-C1INH; HAE with normal C1 inhibit
Plasmin is a natural trigger for bradykinin production in patients with hereditary angioedema with factor XII mutations
Keywords: جستجو; Angioedema; bradykinin; Factor XII; plasma kallikrein; kininogen; C1 esterase inhibitor; plasmin; εACA; ε-Aminocaproic acid; C1inh; C1 esterase inhibitor; FXII; Factor XII; FXIIa; Active Factor XII; HAE; Hereditary angioedema; HBS; HEPES-buffered saline
Embolization of Metastatic Neuroendocrine Tumor Resulting in Clinical Manifestations of Syndrome of Inappropriate Secretion of Antidiuretic Hormone
Keywords: جستجو; ADH; antidiuretic hormone; HAE; hepatic artery embolization; NET; neuroendocrine tumor; SIADH; syndrome of inappropriate secretion of antidiuretic hormone;
Comparison of Chromogenic and ELISA Functional C1 Inhibitor Tests in Diagnosing Hereditary Angioedema
Keywords: جستجو; Hereditary angioedema; C1 inhibitor; Complement testing; C1 INH; C1 inhibitor; HAE; Hereditary angioedema;
ELISA to measure neutralizing capacity of anti-C1-inhibitor antibodies in plasma of angioedema patients
Keywords: جستجو; NAbs; neutralizing antibodies; C1-inh; C1-inhibitor; AAE; acquired angioedema; HAE; hereditary angioedema; NC%; percentage neutralizing capacity; Auto-autoantibodies; Acquired angioedema; Hereditary angioedema; C1-inhibitor deficiency;
Recombinant Human-C1 Inhibitor Is Effective and Safe for Repeat Hereditary Angioedema Attacks
Keywords: جستجو; Hereditary angioedema; Recombinant human C1 esterase inhibitor; Repeat attacks; C1INH; C1 Esterase inhibitor; HAE; Hereditary angioedema; HRI; Host-related impurities; IS; Investigator Score; OLE; Open-label extension; rhC1INH; Recombinant human C1 estera
C1-inhibitor polymers activate the FXII-dependent kallikrein-kinin system: Implication for a role in hereditary angioedema
Keywords: جستجو; BSA; bovine serum albumin; C1-inh; complement C1 esterase inhibitor; C1PIV; in vivo sized C1-inh polymers; CPDA; citrate phosphate dextrose adenine; CPK; chromozyme PK; FXII; coagulation factor XII; FXIIa; activated FXII; dBSA; heat denatured BSA; HAE; he
Characterization of patients with angioedema without wheals: The importance of F12 gene screening
Keywords: جستجو; C1-INH; C1 inhibitor; HAE; hereditary angioedema; FXII-HAE; hereditary angioedema with factor XII mutation; U-HAE; hereditary angioedema with unknown genetic mutation; InH-AAE; idiopathic non-histaminergic acquired angioedema; SERPING1; serpin peptidase i
Original ArticleCharacterization of Anaphylaxis After Ecallantide Treatment of Hereditary Angioedema Attacks
Keywords: جستجو; Hypersensitivity; Anaphylaxis; Allergy; Hereditary angioedema; Ecallantide; HAE; -; Negative; +; Positive; Anti-ecal IgE; anti-ecallantide IgE antibody; Anti-P pastoris IgE; anti-P pastoris IgE antibody; bp; Blood pressure; D5W; 5% dextrose in water
Serosal cuticle formation and distinct degrees of desiccation resistance in embryos of the mosquito vectors Aedes aegypti, Anopheles aquasalis and Culex quinquefasciatus
Keywords: جستجو; EDR; embryonic desiccation resistance; HAE; hours after egg laying; SC; serosal cuticle; Desiccation resistance; Serosal cuticle; Embryogenesis; Mosquito vectors; Impermeability; Viability under dry conditions;
When mothers anticipate: Effects of the prediapause stage on embryo development time and of maternal photoperiod on eggs of a temperate and a tropical strains of Aedes albopictus (Diptera: Culicidae)
Keywords: جستجو; HAE; hour after egg laying; LD; long daylight; SD; short daylight; Embryo development; Diapause; Day length; Phenotypic plasticity;
Mutations analysis of C1 inhibitor coding sequence gene among Portuguese patients with hereditary angioedema
Keywords: جستجو; HAE; C1-INH; Mutations; SERPING1 gene;
Factor XII-independent activation of the bradykinin-forming cascade: Implications for the pathogenesis of hereditary angioedema types I and II
Keywords: جستجو; Bradykinin; factor XII; prekallikrein; kininogen; C1 inhibitor; APMSF; (p-Amidinophenyl)methanesulfonyl fluoride; C1-INH; C1 inhibitor; CTI; Corn trypsin inhibitor; HAE; Hereditary angioedema; HK; High-molecular-weight kininogen; Hsp90; Heat shock protein
Nanofiltered C1-Esterase Inhibitor for the Acute Management and Prevention of Hereditary Angioedema Attacks due to C1-Inhibitor Deficiency in Children
Keywords: جستجو; C1 INH-nf; Nanofiltered C1-esterase inhibitor; C1 INH; C1-esterase inhibitor; HAE; Hereditary angioedema;
Identification of a novel and recurrent mutation in the SERPING1 gene in patients with hereditary angioedema
Keywords: جستجو; C1-INH, C1 inhibitor; HAE, Hereditary angioedema; HRM, High resolution melting; PCR, Polymerase chain reaction; SERPING1, Serpin peptidase inhibitor clade G, member 1.Hereditary angioedema; C1-inhibitor; Founder effect; Mutation; SERPING1; HAE
Hereditary Angioedema with Normal C1-INH (HAE Type III)
Keywords: جستجو; Hereditary angioedema; normal C1-INH; type III; estrogen; diagnosis; treatment; factor XII mutation; ACE; Angiotensin-converting enzyme; C1-INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-C1-INHdef; Hereditary angioedema due to C1 inhibitor deficienc