Keywords: لامین; Lamin; Progeria; Atherosclerosis; Menarche; Puberty;
مقالات ISI لامین (ترجمه نشده)
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Keywords: لامین; Left atrial function; Left atrial function index; Cardiovascular diseases; Atrial fibrillation; Epidemiology; Echocardiography; CVD; Cardiovascular disease; LA; Left atrial; LAFI; Left atrial function index; LAmax; Maximum left atrial volume; LAmin; Minim
Keywords: لامین; Matrix metalloproteinase-2; Nucleus; Myocardial ischemia; Reperfusion; Proteolysis; Lamin;
Keywords: لامین; Nuclear envelope; Lamin; Nuclear membrane; Muscular dystrophy; Dystonia;
Keywords: لامین; Anti-neutrophil cytoplasmic antibodies; Autoantibodies; Human umbilical vein endothelial cell; Vasculitides; Lamin; Erk;
Keywords: لامین; Echocardiography; Real-time three-dimensional echocardiography; Left atrial volume; Comparison; AL; Biplane area-length method; CI; Confidence interval; LA; Left atrial; LAmax; Maximum left atrial volume at end-systole; LAmin; Minimum left atrial volume a
Keywords: لامین; Chromatin; Nuclear lamina; Lamin; Nuclear pore complex; Nucleoporin; Nup
Sun-mediated mechanical LINC between nucleus and cytoskeleton regulates βcatenin nuclear access
Keywords: لامین; Sun; Nesprin; Lamin; LINC; Nucleoskeleton; Nuclear envelope; βcatenin; Bone; Adipogenesis; Mechanical signals; Mesenchymal stem cells;
Mice overexpressing lamin B1 in oligodendrocytes recapitulate the age-dependent motor signs, but not the early autonomic cardiovascular dysfunction of autosomal-dominant leukodystrophy (ADLD)
Keywords: لامین; ADLD; adult-onset autosomal dominant leukodystrophy; BRS; index of cardiac baroreflex sensitivity; EEG; electroencephalogram; EMG; electromyogram; HP; heart period; LMNB1; lamin B1 gene; N; non-rapid-eye-movement sleep; PBS; phosphate buffered saline; Plp
Abnormal nuclear morphology is independent of longevity in a zmpste24-deficient fish model of Hutchinson-Gilford progeria syndrome (HGPS)
Keywords: لامین; CMV; cytomegalovirus; DDR; DNA damage response; GFP; green fluorescent protein; Gy; gray; H2B; histone H2B; n.s.; not significant; qPCR; quantitative polymerase chain reaction; s.d.; standard deviation; zmpste24; zinc metallopeptidase, STE24 homolog; Lami
Abnormal retention of nuclear lamina and disorganization of chromatin-related proteins in spermatozoa from DPY19L2-deleted globozoospermic patients
Keywords: لامین; BAF; BAF-L; Globozoospermia; Lamin; Nuclear lamina; Spermiogenesis;
Macrocyclic MEK1/2 inhibitor with efficacy in a mouse model of cardiomyopathy caused by lamin A/C gene mutation
Keywords: لامین; Cardiomyopathy; Emery-Dreifuss muscular dystrophy; Extracellular signal-regulated kinase; Lamin; MEK inhibitor; Mitogen-activated protein kinase;
New intronic splicing mutation in the LMNA gene causing progressive cardiac conduction defects and variable myopathy
Keywords: لامین; EDMD; Emery-Dreifuss Muscular Dystrophy; CCD; cardiac conduction defect; VUCS; variant of unknown clinical significance; CK; creatine phosphokinase; AVB; atrioventricular block; PM; pacemaker; Lamin; Lamin A/C-dependent limb-girdle muscular dystrophy type
MTHFD1 regulates nuclear de novo thymidylate biosynthesis and genome stability
Keywords: لامین; MTHFD1; SHMT; TYMS; DHFR; Thymidylate; Folate; Lamin; DNA replication; Multi-enzyme complex; FOCM; folate-mediated one-carbon metabolism; MTHFD1; methylenetetrahydrofolate dehydrogenase 1; SHMT1; cytoplasmic serine hydroxymethyltransferase; TYMS; thymidyl
A rare mutation in MYH7 gene occurs with overlapping phenotype
Keywords: لامین; MYH7; Left ventricular non-compation; Cardiomyopathy; FTD; Laing Distal Myopathy; Overlapping syndrome; ACTA1; actin 1; CPK; creatine phosphokinase; CFTD; Congenital Fiber Type Disproportion; COX; cytochrome C oxidase; DES; desmin; EMG; electromyography;
Evolution of centrosomes and the nuclear lamina: Amoebozoan assets
Keywords: لامین; LINC complex; Sun1; Nuclear lamina; Lamin; Nuclear envelope; Centrosome; Basal body; Centriole; LEM-domain
Peptidic tools applied to redirect alternative splicing events
Keywords: لامین; ANP; atrial natriuretic peptide; ASBNP; alternatively spliced BNP; ASO; antisense oligonucleotides; BNP; B-type natriuretic peptide; CBD; calmodulin binding domain; CPP; cell penetrating peptides; DMD; Duchenne muscular dystrophy; ESE; exonic splicing enh
Mitogen-activated protein kinase kinase 1/2 inhibition and angiotensin II converting inhibition in mice with cardiomyopathy caused by lamin A/C gene mutation
Keywords: لامین; Lamin; Cardiomyopathy; Nuclear envelope; Mitogen-activated protein kinase;
Lamins of the sea lamprey (Petromyzon marinus) and the evolution of the vertebrate lamin protein family
Keywords: لامین; Petromyzon marinus; Sea lamprey; Agnatha; Gnathostomata; Chondrichthyes; Lamin; Gene neighborhood; Vertebrate evolution
The cephalochordate Branchiostoma genome contains 26 intermediate filament (IF) genes: Implications for evolution of chordate IF proteins
Keywords: لامین; Cephalochordates; Branchiostoma; Intermediate filament; Lamin; Phylogeny
Postage for the messenger: designating routes for nuclear mRNA export
Keywords: لامین; mRNA export; nuclear envelope; nuclear pore complex; transport; exportin; lamin
In vitro characterization of the RS motif in N-terminal head domain of goldfish germinal vesicle lamin B3 necessary for phosphorylation of the p34cdc2 target serine by SRPK1
Keywords: لامین; SRPK1; CLK; Lamin; Germinal vesicle; SR-protein; Goldfish; Fugu; Tetraodon; Phosphorylation; ASF/SF2; alternative splicing factor/splicing factor 2; CLK; cdc2-like kinase; GV; germinal vesicle; LB3; lamin B3; RS repeat; arginine/serine repeat; SRPK1; seri
N-terminal Pro brain natriuretic peptide is a reliable biomarker of reduced myocardial contractility in patients with lamin A/C gene mutations
Keywords: لامین; Lamin; Genetic cardiomyopathy; NT-proBNP; Heart failure; Left ventricular dysfunction;
Accumulation of distinct prelamin A variants in human diploid fibroblasts differentially affects cell homeostasis
Keywords: لامین; Lamin; Prelamin A; Aging; Nucleus; Laminopathies; Disease;
Subcellular localization of SREBP1 depends on its interaction with the C-terminal region of wild-type and disease related A-type lamins
Keywords: لامین; Lamin; SREBP1; Nuclear envelope; Lipodystrophy; Progeria
Pharmacological inhibition of c-Jun N-terminal kinase signaling prevents cardiomyopathy caused by mutation in LMNA gene
Keywords: لامین; Cardiomyopathy; Lamin; MAP kinase; JNK; Emery–Dreifuss muscular dystrophy
Attenuated hypertrophic response to pressure overload in a lamin A/C haploinsufficiency mouse
Keywords: لامین; Lamin; Hypertrophy; Mechanical stress; Pressure overload; Mechanotransduction; Transverse aortic constriction;
Reduced expression of A-type lamins and emerin activates extracellular signal-regulated kinase in cultured cells
Keywords: لامین; ERK, extracellular signal-regulated kinase; JNK, c-Jun-N-terminal kinase; MAPK, mitogen-activated protein kinase; MEK, MAPK/ERK kinase; OD, optical densityNuclear envelope; Nuclear lamina; Lamin; Emerin; Emery-Dreifuss muscular dystrophy
Herpes simplex virus 2 UL13 protein kinase disrupts nuclear lamins
Keywords: لامین; Herpes simplex virus; HSV-2; UL13; Lamin; Phosphorylation; Nuclear; Egress
Nuclear protein import is reduced in cells expressing nuclear envelopathy-causing lamin A mutants
Keywords: لامین; Lamin; Hutchinson Gilford progeria syndrome (HGPS); Restrictive dermopathy (RD); Nuclear protein transport; Nuclear localization sequence (NLS); Importin; Nuclear pore complex (NPC); Fluorescence recovery after photobleaching (FRAP); Nucleoporin 153 (Nup1
Centrosome attachment to the C. elegans male pronucleus is dependent on the surface area of the nuclear envelope
Keywords: لامین; Nuclear envelope; Centrosome; Male pronucleus; Pronuclear migration; Lamin; LEM; BAF; Microtubule aster; Outer nuclear membrane; Dynein
Muscle dystrophy single point mutation in the 2B segment of lamin A does not affect the mechanical properties at the dimer level
Keywords: لامین; Laminopathy; Lamin; Muscle dystrophy; Nanomechanics; Mechanical properties; Deformation; Plasticity; Fracture; Nuclear envelope; Stress–strain; Young's modulus
The epigenetics of nuclear envelope organization and disease
Keywords: لامین; Nuclear envelope; Lamin; Inner nuclear membrane protein; Epigenetics; Position effect; Heterochromatin
Accelerated telomere shortening and replicative senescence in human fibroblasts overexpressing mutant and wild-type lamin A
Keywords: لامین; Lamin; Laminopathies; Progeroid syndromes; Hutchison-Gilford Progeroid Syndrome; Aging
The nuclear envelope as an integrator of nuclear and cytoplasmic architecture
Keywords: لامین; Nuclear envelope; Lamin; Nesprin; SUN proteins; Cytoskeleton; Actin
The effects of the Cox maze procedure on atrial function
Keywords: لامین; AF; atrial fibrillation; BSA; body surface area; LA; left atrium; LAA; left atrial appendage; LAAE; left atrial active emptying percentage of total emptying; LAAEI; left atrial active emptying index; LACC; left atrial volume change; LAEF; left atrial acti
A structure–activity relationship study of siRNAs with structural variations
Keywords: لامین; RNA interference (RNAi); Small interfering RNA (siRNA); Lamin; Structure–activity relationship; Off-target gene silencing; Innate immune response; OAS2; Dicer
The prelamin A pre-peptide induces cardiac and skeletal myoblast differentiation
Keywords: لامین; Lamin; Cytoskeleton; Differentiation; Farnesylation; Muscular dystrophy; Cardiomyopathy;
Les lipodystrophies primitives
Keywords: لامین; Insulin resistance; Hyperandrogenism; Dyslipidemia; Diabetes; Lamin; PPARγ; Seipin; AGPAT2Insulinorésistance; Hyperandrogénie; Dyslipidémie; Diabète; Lamine; PPARγ; Seipine; AGPAT2
“Laminopathies”: A wide spectrum of human diseases
Keywords: لامین; Lamin; Nuclear envelope; Intermediate filaments; Muscular dystrophy; Lipodystrophy; Progeria
A-type lamin networks in light of laminopathic diseases
Keywords: لامین; Cell cycle; Chromosome; Differentiation; Laminopathy; Lamin; Transcription factor
Inner nuclear membrane and regulation of Smad-mediated signaling
Keywords: لامین; Nuclear envelope; Inner nuclear membrane; MAN1; Lamin; Transforming growth factor-beta; Bone morphogenic protein
Proteasome-mediated degradation of integral inner nuclear membrane protein emerin in fibroblasts lacking A-type lamins
Keywords: لامین; Nuclear envelope; Lamin; Emerin; Nesprin; Proteasome; Muscular dystrophy;
The nuclear lamina and its proposed roles in tumorigenesis: Projection on the hematologic malignancies and future targeted therapy
Keywords: لامین; Aging; Apoptosis; Cancer; Chromatin; Lamin; Laminopathies; Nuclear envelope
Sequence divergence of coiled coils—structural rods, myosin filament packing, and the extraordinary conservation of cohesins
Keywords: لامین; Coiled coils; SMC; Cohesin; Condensin; Myosin; Giantin; NuMA; Desmin; Lamin; Kinesin; Evolution
The Drosophila melanogaster LEM-domain protein MAN1
Keywords: لامین; Drosophila; MAN1; LEM-domain proteins; Lamin; Bocksbeutel; Nuclear envelope
Polyethyleneimine as a transmembrane carrier of fluorescently labeled proteins and antibodies
Keywords: لامین; Polyethyleneimine; PEI; Protein delivery; Avidin; Alexa-avidin conjugates; Lamin; Glial cells; Fibroblasts; Antibody delivery; Protein carrier; Fluorescent detection;
Apical cell adhesion molecule, trophinin, localizes to the nuclear envelope
Keywords: لامین; PCR, polymerase chain reaction; SDS–PAGE, sodium dodecyl sulfate polyacrylamide gel electrophoresis; GFP, green fluorescent protein; NE, nuclear envelopeTrophinin; Magphinin; Nuclear envelope; Nuclear matrix; Lamin
A-type nuclear lamins, progerias and other degenerative disorders
Keywords: لامین; Lamin; Progeria; Nuclear organization; Dystrophic syndromes;