The effects of sapropterin on urinary monoamine metabolites in phenylketonuria
Keywords: تیروزین هیدروکسیلاز; PKU; Phenylketonuria; PAH; Phenylalanine hydroxylase; TH; Tyrosine hydroxylase; LNAA; Large neutral amino acids; MA; Monoamines; HPLC; High-Performance Liquid Chromatography; DA; Dopamine; DOPAC; Dihydroxyphenylacetate; E; Epinephrine; 5HIAA; 5-hydroxyind