Keywords: سندرم غرب; West syndrome; Epileptic spasms; Secondary prevention;
مقالات ISI سندرم غرب (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: سندرم غرب; DEE; developmental and epileptic encephalopathy; EEG; electroencephalography; EIMFS; epilepsy of infancy with migrating focal seizures; EMAS; epilepsy with myoclonic atonic seizures; ID; intellectual disability; IQR; interquartile range; KD; ketogenic die
Keywords: سندرم غرب; Adrenocorticotropic hormone; Epilepsy; Epileptic spasms; Valproate; Vigabatrin; Vitamin B6; West syndrome;
Keywords: سندرم غرب; Epileptic encephalopathy; Neuronal auto-antibodies; West syndrome; Lennox-Gastaut syndrome; Immune-mediated epilepsy;
Keywords: سندرم غرب; Benign neonatal seizures; Cerebral palsy; Rolandic spike; Occipital epilepsy; West syndrome;
Keywords: سندرم غرب; infantile spasms; West syndrome; hypsarrhythmia; steroid; methylprednisolone; short-term outcome;
Keywords: سندرم غرب; infantile spasms; West syndrome; hypsarrhythmia; ACTH; prednisolone;
Keywords: سندرم غرب; Ketosis; Hypsarrhythmia; EEG; West syndrome; Infantile spasms;
Keywords: سندرم غرب; EEG; ACTH therapy; West syndrome; Seizure outcome; Epileptic discharges; Prediction of seizure relapse
Keywords: سندرم غرب; Epileptic encephalopathy; West syndrome; Involuntary movement; Hyperkinetic movement; Hand stereotype; Whole-exome sequencing
Keywords: سندرم غرب; West syndrome; Infantile spasm; Prognosis; Epilepsy
Keywords: سندرم غرب; West syndrome; Severe combined immunodeficiency syndrome; CD4/8; Hematopoietic stem cell transplantation; Intravenous injection of immunoglobulin
Keywords: سندرم غرب; Epileptic encephalopathy; Ketogenic diet; Steroid; West syndrome; Encephalopathy with CSWS;
Keywords: سندرم غرب; infantile spasms; West syndrome; topiramate; pediatric; epilepsy
Keywords: سندرم غرب; West syndrome; Heart rate variability; Autonomic function; Infantile spasms; Hypsarrhythmia
Keywords: سندرم غرب; WS; West syndrome; PET; positron emission tomography; EEG; electroencephalogram; ED; epileptiform discharges; AEDs; antiepileptic drugs; MISF; multifocal independent spike foci; SF; seizure-free; No-SF; no seizure-free; West syndrome; EEG; Seizures; Progn
Keywords: سندرم غرب; infantile spasms; West syndrome; hypsarrhythmia; ACTH; prednisolone; treatment
Keywords: سندرم غرب; Epilepsy; West syndrome; HFOs; Hypsarrhythmia; Anticonvulsant;
Keywords: سندرم غرب; West syndrome; Infantile spasms syndrome; CDKL5; STXBP1; MEF2C; SCN2A
Keywords: سندرم غرب; West syndrome; Dravet syndrome; mTOR; Epilepsy; Cognition; SUDEP; Arx; GABA; Sodium channels; Multiple-hit model; GABA; NMDA; Tetrodotoxin
Keywords: سندرم غرب; Glutaric aciduria; Maple syrup urine disease; Epileptic encephalopathy; West syndrome
Keywords: سندرم غرب; West syndrome; Down syndrome; Hypsarrhythmia; Prognosis;
Keywords: سندرم غرب; Tuberous sclerosis complex; TSC1; TSC2; Angiomyolipomas; West syndrome
Keywords: سندرم غرب; Infantile spasms; West syndrome; Aetiology
Keywords: سندرم غرب; Sweep visual evoked potentials; Childhood epilepsy; West syndrome; Grating visual acuity; Cortical visual impairment; Nystagmus; Strabismus
Keywords: سندرم غرب; Infantile spasms; West syndrome; Hypsarrhythmia; Genetics; Treatment
Keywords: سندرم غرب; West syndrome; hypsarrhythmia; prednisolone; ACTH;
Keywords: سندرم غرب; Long-term weekly ACTH therapy; West syndrome; Tuberous sclerosis complex; Relapse; Epileptic spasms; Hypsarrhythmia
Keywords: سندرم غرب; West syndrome; Bilateral independence; Epileptic spasms; Callosotomy
Keywords: سندرم غرب; STXBP1-related epileptic encephalopathy; Ohtahara syndrome; West syndrome; Loss-of-function
Novel IARS2 mutations in Japanese siblings with CAGSSS, Leigh, and West syndrome
Keywords: سندرم غرب; CAGSSS; Whole-exome sequencing; Leigh syndrome; West syndrome; Mitochondrial disease;
A novel STXBP1 mutation causes typical Rett syndrome in a Japanese girl
Keywords: سندرم غرب; Typical Rett syndrome; STXBP1mutation; West syndrome; Japanese girl;
SÃndrome de West criptogénico: perfil clÃnico, respuesta al tratamiento y factores pronósticos
Keywords: سندرم غرب; SÃndrome de West; Espasmos infantiles; Criptogénico; EtiologÃa; Vigabatrina; Factores pronósticos; West syndrome; Infantile spasms; Cryptogenic; Aetiology; Vigabatrin; Prognostic factors;
Cryptogenic West syndrome: Clinical profile, response to treatment and prognostic factors
Keywords: سندرم غرب; West syndrome; Infantile spasms; Cryptogenic; Aetiology; Vigabatrin; Prognostic factors; SÃndrome de West; Espasmos infantiles; Criptogénico; EtiologÃa; Vigabatrina; Factores pronósticos;
Strength and stability of EEG functional connectivity predict treatment response in infants with epileptic spasms
Keywords: سندرم غرب; Brain network; Hypsarrhythmia; BASED score; West syndrome; Electroencephalography; Adrenocorticotropic hormone (ACTH); Infantile spasms;
Clinical and laboratory observationsLegionella pneumophila Pneumonia in Two Infants Treated with Adrenocorticotropic Hormone
Keywords: سندرم غرب; infantile spasms; West syndrome; ACTH; Adrenocorticotropic hormone;
Case ReportTotal corpus callosotomy for epileptic spasms after acute encephalopathy with biphasic seizures and late reduced diffusion (AESD) in a case with tuberous sclerosis complex
Keywords: سندرم غرب; Corpus callosotomy; Epileptic spasms; West syndrome; Acute encephalopathy with biphasic seizures and late reduced diffusion; Tuberous sclerosis complex;
Case ReportClinical features of a female with WDR45 mutation complicated by infantile spasms: a case report and literature review
Keywords: سندرم غرب; Beta-propeller protein-associated neurodegeneration; WDR45; Infantile spasms; West syndrome; Adrenocorticotropic hormone therapy;
Diagnosis, treatment, and outcomes of infantile spasms in the Trisomy 21 population
Keywords: سندرم غرب; Infantile spasms; Epileptic spasms; Trisomy 21; Down syndrome; West syndrome; Idiopathic infantile spasms;
Recognition of Infantile Spasms Is Often Delayed: The ASSIST Study
Keywords: سندرم غرب; infantile spasms; West syndrome; diagnosis; delay; EEG; Electroencephalography;
Original articleFast (40-150Â Hz) oscillations are associated with positive slow waves in the ictal EEGs of epileptic spasms in West syndrome
Keywords: سندرم غرب; High-frequency oscillations; Fast oscillations; West syndrome; Infantile spasms; Slow wave; Ictal EEG;
Antibodies against peptides of NMDA-type GluR in cerebrospinal fluid of patients with epileptic spasms
Keywords: سندرم غرب; West syndrome; Infantile spasms; Autoantibodies; Cognitive outcome; Motor outcome;
Visual impairment in FOXG1-mutated individuals and mice
Keywords: سندرم غرب; FOXG1, Forkead Box G1; GCL, ganglion cell layer; RBPMS, anti-RNA-binding protein; RTT, Rett SyndromeRett syndrome; autism; west syndrome; visual cortex; inhibitory interneurons; cortical blindness
Epileptic spasms in clusters with focal EEG paroxysms: A study of 12 patients
Keywords: سندرم غرب; Clusters; Encephalopathy; Epileptic spasms; Focal hypsarrhythmia; surgery; West syndrome;
Perceived efficacy of cannabidiol-enriched cannabis extracts for treatment of pediatric epilepsy: A potential role for infantile spasms and Lennox-Gastaut syndrome
Keywords: سندرم غرب; Cannabis; Marijuana; Cannabidiol; Survey; Infantile spasms; West syndrome; Lennox-Gastaut syndrome;
Original articleChromosomal microarray in unexplained severe early onset epilepsy - A single centre cohort
Keywords: سندرم غرب; Infantile spasms; West syndrome; Epilepsy; Epileptic encephalopathy;
LAMA2-related congenital muscular dystrophy complicated by West syndrome
Keywords: سندرم غرب; Congenital muscular dystrophy; LAMA2; Laminin α2 deficiency; West syndrome
Psychomotor development following early treatment of severe infantile vitamin B12 deficiency and West syndrome – Is everything fine? A case report and review of literature
Keywords: سندرم غرب; Infantile vitamin B12 deficiency; Brain damage; Psychomotor development; West syndrome; Infantile spasms syndrome; Neurodevelopmental delay; Long-term follow-up
Ketogenic diet therapy can improve ACTH-resistant West syndrome in Japan
Keywords: سندرم غرب; West syndrome; ACTH; Ketogenic diet; Gastrointestinal side effects
Improving the inter-rater agreement of hypsarrhythmia using a simplified EEG grading scale for children with infantile spasms
Keywords: سندرم غرب; Ð; Fleiss' kappa; BASED; Burden of Amplitudes and Epileptiform Discharges; Infantile spasms; West syndrome; Electroencephalogram; EEG; Epileptic encephalopathy; BASED score;