Keywords: ABC; ATP Binding Cassette; AE; anion exchanger; ASL; airways surface liquid; ATP; adenosine triphosphate; CAP; channel activating protease; CaCC; calcium activated chloride channel; CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regu
مقالات ISI (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: potentiator; corrector; read-through; CFTR;
Keywords: ABTS; 2,2â², azinobis(3-ethylbenzothiazoline-6-sulfonic acid); ANOVA; analysis of variance; bLPO; bovine lactoperoxidase; CFTR; cystic fibrosis transmembrane conductance regulator; DMSO; dimethyl sulfoxide; DUOX-2; dual oxidase; DTNB; 5,5â²-dithiobis-(2
Keywords: CO; carbonmonoxide; -CN; cyanide; CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane regulator; C; one-letter abbreviation for cysteine; Cys; cysteine; -SCys; cysteinate; Cys-SOH; cysteine sulfenic acid; Cys-SO2-; cysteine sulfinic acid; Cys-S
Keywords: CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; CRD; Centre of Research and Dissemination; DNA; deoxyribonucleic acid; HAS; Haute Autorité de Santé; HTA; health technology assessment; ICER; incremental cost effectiveness
Keywords: AI; anterior intestine; PI; posterior intestine; IF; intestinal fluid; GIT; gastrointestinal tract; TMT; tandem mass tag; ppt; parts per thousand; LFQ; label free quantitation; ACE; angiotensin converting enzyme; HSC70; heat shock cognate 71â¯kDa protein
Keywords: α-CGRP; alpha-calcitonin gene related peptide; Ang; angiopoietin; AE2; anion exchanger 2; ADP; adenosine diphosphate; ADPKD; autosomal dominant polycystic kidney disease; ATP; adenosine triphosphate; ASBT; sodium-dependent bile acid transporter; AQP; aqu
Keywords: Ion Transport; Diarrhea; Enteric Pathogen; Epithelium; ATP; adenosine triphosphate; ATPase; adenosine triphosphatase; cAMP; adenosine 3â²,5â²-cyclic monophosphate; CDI; Clostridium difficile infection; CFTR; cystic fibrosis transmembrane conductance reg
Keywords: Cystic fibrosis; Protein species; Proteomics; Laminopathies; Acute exacerbation; CFTR; Enrichment analysis;
Keywords: Hereditary pancreatitis; Familial pancreatitis; Genetic evaluation; Genetic variants associated with pancreatitis; PRSS1; SPINK1; CFTR;
Keywords: ABCA1 gene; Tangier disease; Male infertility; Spermatogenesis; Hormonal axis; High-density lipoprotein; FHA; hypoalphalipotroteinemia; CFTR; Cystic Fibrosis Transmembrane Conductance Regulator; FHS; follicle stimulating hormone; LH; luteinizing hormone;
Keywords: Chloride Secretion; Bicarbonate Secretion; DRA; Ion Transport; AE2; anion exchanger 2; CA; carbonic anhydrase; cAMP; cyclic adenosine monophosphate; CFTR; cystic fibrosis transmembrane conductance regulator; ÎIsc; change in short-circuit current; DRA; d
Keywords: RDC; reactive ductular cell; DAMPs; danger associated molecular patterns; PAMPs; pathogen associated molecular patterns; cAMP; cyclic adenosine monophosphate; NOS; nitric oxide synthase; RNOS; reactive nitrogen oxide species; CFTR; cystic fibrosis transme
Keywords: Polycystic kidney disease; Fluid secretion; Liver X receptor; mTOR; Extracellular signal-regulated kinases; CFTR;
Keywords: DNA; deoxyribonucleic acid; PCR; polymerase chain reaction; CF; cystic fibrosis; CBAVD; congenital bilateral absence of the vas deferens; CFTR; cystic fibrosis transmembrane conductance regulator; ICSI; intracytoplasmic sperm injection; SNP; single nucleo
Keywords: Channelopathy; Animal venom; Peptide toxin; Disease; Ligand-receptor interaction; Drug seeds; ASIC; acid-sensing ion channel; ATP; adenosine triphosphate; BK channel; big potassium channel; CFA; Freund's complete adjuvant; CFTR; cystic fibrosis transmembr
Keywords: AANAT; arylalkylamine N-acetyltransferase; AE2; Clâ/HCO3- anion exchanger 2; ANIT; α-naphthylisothiocyanate; BA; biliary atresia; BDL; bile duct ligation; cAMP; adenosine 3â²,5â²-cyclic monophosphate; CCA; cholangiocarcinoma; CCl4; carbon tetrachlo
Keywords: ASBT; apical sodium-dependent bile acid transporter; ASDs; amorphous solid dispersions; BACS; bile acid-CoA synthase; BAT; bile acid-amino acid transferase; BCS; biopharmaceutics classification system; BSH; bile salt hydrolase; C4; 7α-hydroxy-4-cholesten
Keywords: dziedziczne zapalenie trzustki; gen PRSS1; CFTR; wirus Epsteina i Barr; Hereditary pancreatitis; PRSS1 gene; CFTR gene; Epstein-Barr virus;
Keywords: AST; aspartate aminotransferase; ALT; alanine aminotransferase; CFTR; cystic fibrosis transmembrane conductance regulator; GGT; gamma-glutamyltranspeptidase; ULN; upper limit of normal; Cystic fibrosis liver disease; Newborn screening;
Keywords: Knee; Tumor resection; Combined distal femur proximal tibia reconstruction; CFTR; combined distal femur and proximal tibia replacement; ISOLS; International Society of Limb Salvage; KMFTR; Kotz Modular Femur and Tibia Reconstruction system; HMRS; Howmedic
Keywords: Ionocyte; Opercular epithelium; CFTR; NKCC; Eurythermic; Euryhaline; Adrenergic; Hypotonic; Hypertonic;
Keywords: low birth weight; prematurity; preterm birth; small for gestational age; infant mortality; CF; Cystic fibrosis; CFTR; CF transmembrane regulator; ICD-9; International Classification of Diseases, Ninth Revision; SGA; Small for gestational age; LBW; Low bir
Keywords: CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; MSD; membrane-spanning domain; NBD; nucleotide-binding domain; FEV1; forced expiratory volume in 1Â s; Cystic fibrosis; CFTR; Potentiator; Corrector; CFTR modulator; Read-thro
Keywords: Pancreatitis; Pancreatic cystosis, cystic fibrosis; CFTR;
Keywords: Cystic fibrosis; Gut microbiota; Antioxidant vitamins; Inflammation; 16ss rDNA; 16 small subunit ribosomal DNA; CD; Crohn's disease; CFRD; cystic fibrosis-related diabetes; CFTR; cystic fibrosis transmembrane regulator; CVD; cardiovascular disease; ENaC;
Keywords: immunoreactive trypsinogen; intestinal current measurement; nasal potential difference; newborn screening; sweat chloride; CF; Cystic fibrosis; CFFPR; CF Foundation Patient Registry; CFSPID; CF screen positive, inconclusive diagnosis; CFTR; CF transmembra
Keywords: BMI; Body mass index; CF; Cystic fibrosis; CFRD; Cystic fibrosis-related diabetes; CFTR; Cystic fibrosis transmembrane conductance regulator; CI; Confidence interval; FEV1% predicted; Forced expiratory volume in one second; FVC % predicted; Forced vital c
Keywords: inconclusive screening results; mixed methods; maternal experience; CF; Cystic fibrosis; CFTR; Cystic fibrosis transmembrane regulator; IRT; Immunoreactive trypsinogen; NBS; Newborn screening; RR; Response rate;
Keywords: CFTR-related disorder; cystic fibrosis; genotype; mutation; penetrance; variant; atypical CF; adult diagnosis of CF; CF; Cystic fibrosis; CFTR; CF transmembrane conductance regulator; CFTR2; Clinical and functional translation of CFTR; CT; Computed tomogr
Keywords: chronic pancreatitis; acute recurrent pancreatitis; PRSS1; SPINK1; CFTR; next-generation sequencing; ATP8B1; ATPase type 8B member 1; CASR; Calcium-sensing receptor; CFTR; Cystic fibrosis transmembrane conductance regulator gene; CLDN2; CLAUDIN 2; CP; Chr
Keywords: BMI; body mass index; CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane regulator; CI; confidence interval; CLAD; chronic lung allograft dysfunction; CT; computed tomography; FEV1; forced expiratory volume in one second; GERD; gastroesophageal refl
Keywords: Mucoviscidosis; Cystic fibrosis; Bicarbonate; Mucus; Cystic fibrosis transmembrane conductance regulator; CFTR;
Keywords: cystic fibrosis transmembrane conductance regulator; growth; lung function; Australia; BMI; Body mass index; CF; Cystic fibrosis; CFSPID; CF screen positive inconclusive diagnosis; CFTR; CF transmembrane conductance regulator; FEV1%; Forced expiratory vol
Keywords: AJ; adherent junctions; CFTR; cystic fibrosis conductance regulator; ECGF; endothelial cell growth factor; EMV; endothelial microvesicles; eNOS; endothelial nitric oxide synthase; HUVEC; human umbilical vein endothelial cells; PAEC; pulmonary artery endot
Keywords: CF screen positive; inconclusive diagnosis; CFSPID; CFTR; CFTR-related metabolic syndrome; CRMS; ICD-10; ICM; immunoreactive trypsinogen; intestinal current measurement; IRT; nasal potential difference; newborn screening; sweat test; CDC; Centers for Dise
Keywords: AA; arachidonic acid; AMs; alveolar macrophages; BAL; bronchoalveolar lavage; BM; bone marrow; BMDMs; bone marrow-derived macrophages; CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; DHA; docosahexaenoic acid; G-CSF; granul
Keywords: CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; PWCF; patients with CF; CD11b; integrin alpha-M; MβCD; methyl-β-cyclodextrin; CXCL; C-X-C Motif Chemokine Ligand; TNF-α; tumor necrosis factor alpha; sTNFR1; soluble TNF re
Keywords: AQP; aquaporins; BDMA; benzyldimethylamine; cDNA; complementary DNA; CFTR; cystic fibrosis transmembrane regulator; DAB; diaminobenzidine; DDSA; dodenyl succinic anhydride; ELISA; enzyme-linked immunosorbent assay; ENaC; epithelial sodium channel; Fgf; fi
Keywords: Cystic fibrosis; Muscle function; Exercise interventions; Aerobic function; CFTR; Nutritional status; Muscle metabolism;
Keywords: AP-1; activator protein 1; BALF; bronchoalveolar lavage fluid; BCL; B-cell lymphoma; CFTR; cystic fibrosis transmembrane conductance regulator; CXCL; chemokine CXC motif ligand; EGR-1; early growth protein 1; FOXO1; forkhead box protein O1; HDAC2; histone
Keywords: ADME; absorption, distribution, metabolism, and excretion; AUC; area under concentration-time curve; BCRP; breast cancer resistance protein; BSEP; bile salt export pump; CFTR; cystic fibrosis transmembrane conductance regulator; Cmax; maximal plasma conce
Keywords: aBMD; Areal bone mineral density; BMD; Bone mineral density; BMI; Body mass index; CF; Cystic fibrosis; CFBD; Cystic fibrosis-related bone disease; CFRD; Cystic fibrosis-related diabetes; CFTR; Cystic fibrosis transmembrane conductance regulator; DMB; Deg
Keywords: CF; cystic fibrosis; BOS; bronchiolitis obliterans syndrome; rRNA; ribosomal small subunit RNA; HIV; human immunodeficiency virus-1; COPD; chronic obstructive pulmonary disease; CFTR; CF transmembrane conductance regulator; BAL; bronchoalveolar lavage; OP
Keywords: AAA; ATPases associated with diverse cellular activities; 17-AAG; 17-N-allylamino-17-demethoxygeldanamycin; ABC; ATP-binding cassette; ABCE1; ATP binding cassette subfamily E member 1; AD; Alzheimer's disease; AIF; apoptosis inducing factor; Akt; Alpha se
Keywords: CFTR; cystic fibrosis; gene therapy; ivacaftor; lung function; Pseudomonas; respiratory tract infection
Keywords: CF; cystic fibrosis; CFRD; cystic fibrosis related diabetes; CFTR; cystic fibrosis transmembrane conductance regulator; DIOS; distal intestinal obstruction syndrome.; Cystic fibrosis; Adenoma; Colon cancer; Colorectal cancer screening;
Keywords: Aspergillus; Aspergillus fumigatus; Aspergillosis; Cystic fibrosis; Allergic bronchopulmonary aspergillosis; CFTR;
Keywords: Cholangiocyte; Laminin 411; Laminin 511; Human induced pluripotent stem cells; Laminin E8 fragment; AQP1; aquaporin 1; BMP; bone morphogenetic protein; BSA; bovine serum albumin; CFTR; cystic fibrosis transmembrane conductance regulator; EGF; epidermal gr
Keywords: Animal model; Cystic fibrosis; CFTR; Lung disease; Pig model;