Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; Haploidentical; Hematopoietic stem cell transplantation; Immunologic deficiency syndromes; Treosulfan;
مقالات ISI بیماری گرانولوماتوز مزمن (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; Liver abscess; Corticosteroids;
Keywords: بیماری گرانولوماتوز مزمن; CF; Cystic fibrosis; CGD; Chronic granulomatous disease; COPD; Chronic obstruction pulmonary disease; CRS; Chronic rhinosinusitis; CVID; Common variable immunodeficiency; PAD; Primary antibody deficiency; PIDD; Primary immunodeficiency disease; TMP-SMX; T
Keywords: بیماری گرانولوماتوز مزمن; CGD; Chronic granulomatous disease; Reduced-intensity conditioning regimen for CGD;
Keywords: بیماری گرانولوماتوز مزمن; Flow cytometry; Intracellular protein; Monoclonal antibody; Primary immunodeficiency disease; Surface protein; ADA; adenosine deaminase; ALPS; autoimmune lymphoproliferative syndrome; APECED; autoimmune polyendocrinopathy-candidiasis-ectodermal dystrop
Keywords: بیماری گرانولوماتوز مزمن; WES; IBD; Neutrophil Oxidative Burst; Genetic Variant; ATP; adenosine triphosphate; CADD; Combined Annotation-Dependent Depletion; CD; Crohn's disease; CGD; chronic granulomatous disease; FMLP; N-formyl-methionyl-leucyl-phenylalanine; GM-CSF; granulocyt
Keywords: بیماری گرانولوماتوز مزمن; APC; antigen presenting cell; CGD; chronic granulomatous disease; DC; dendritic cell; FcγR; Fc gamma receptor; GILT; γ-interferon-inducible lysosomal thiol reductase; GPI; glucose-6-phosphate isomerase; HEL; hen egg lysozyme; IFN-γ; interferon-gamma; I
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; Hematopoietic stem cell transplantation; Unrelated donors; Autoimmune disease; Myeloablative conditioning; Chimerism; Immune reconstitution;
Keywords: بیماری گرانولوماتوز مزمن; Splicing; Alternative splicing; Missplicing; Intron retention; Neutrophil; Granulopoiesis; Severe congenital neutropenia; Chronic granulomatous disease; Myelodysplasia; Acute myeloid leukaemia; Splicing factor;
Keywords: بیماری گرانولوماتوز مزمن; Health care transition; Health care self-management; Pediatric onset chronic illness; Adolescent and young adult; Chronic granulomatous disease;
Keywords: بیماری گرانولوماتوز مزمن; Hematopoietic stem cell transplantation; gammaretroviral vector; lentiviral vector; gene editing; site-specific endonuclease; zinc finger nuclease; CRISPR/Cas9; ADA-SCID; Adenosine deaminase-deficient severe combined immunodeficiency; CGD; Chronic granu
Keywords: بیماری گرانولوماتوز مزمن; Primary immune deficiencies; IgE syndrome; TLRs; Chronic granulomatous disease;
Keywords: بیماری گرانولوماتوز مزمن; Chromobacterium violaceum; Violacein; Chronic granulomatous disease; Gastrointestinal malignancies; Sepsis; Antitumor; Multidrug resistance;
Keywords: بیماری گرانولوماتوز مزمن; Epithelium; Microbiota; Inflammation; Hypoxia-Inducible Factor; Metabolism; ATP; adenosine triphosphatase; CGD; chronic granulomatous disease; DMOG; dimethyloxalylglycine; GI; gastrointestinal; HIF; hypoxia-inducible factor; IBD; inflammatory bowel diseas
Keywords: بیماری گرانولوماتوز مزمن; Glucose-6-phosphate dehydrogenase deficiency; chronic granulomatous disease; neutrophil extracellular trap formation; innate immunity; immunodeficiency; NADPH; CGD; Chronic granulomatous disease; DHR; Dihydrorhodamine 123; G6P; Glucose-6-phosphate; G6PD;
Keywords: بیماری گرانولوماتوز مزمن; Gene therapy; Primary immunodeficiency; Adenosine deaminase deficiency; X-linked severe combined immunodeficiency; Chronic granulomatous disease; Wiskott-Aldrich syndrome;
Keywords: بیماری گرانولوماتوز مزمن; Immunology; primary immunodeficiency; whole-exome sequencing; hematopoietic stem cell transplantation; common variable immunodeficiency; severe combined immunodeficiency; hyper-IgE syndrome; AIP1; Actin-interacting protein 1; APDS; Activated PI3Kδ syndro
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; inflammatory manifestations; mammalian target of rapamycin inhibition; autophagy; inflammasome; IL-17A; IL-1β; APC; Allophycocyanin; CGD; Chronic granulomatous disease; DMSO; Dimethyl sulfoxide; FITC; Fluorescein isothiocya
Keywords: بیماری گرانولوماتوز مزمن; CGD; chronic granulomatous disease; CYBB; cytochrome b beta chain; fMLP; formyl-methionyl-leucyl-phenylalanine; NMD; Nonsense-mediated decay; NOX; NADPH oxidase; PAF; platelet-activating factor; PMA; phorbol-myristate acetate; (P)ESE; (putative) exonic sp
Keywords: بیماری گرانولوماتوز مزمن; Abscess; Suppurative lymphadenitis; Chronic granulomatous disease
Keywords: بیماری گرانولوماتوز مزمن; Primary immunodeficiency; Adults; CGD; Chronic granulomatous disease; CVID; Common variable immune deficiency; HSCT; Hematopoietic stem cell transplant; IVIG; Intravenous immunoglobulin; PID; Primary immune deficiency;
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; hyperinflammation; hematopoietic stem cell; dysfunctional hematopoiesis; competitive repopulation assay; engraftment defect; cell cycle; IL-1β; anakinra; gene therapy; BM; Bone marrow; BrdU; 5-Bromo-2â²-deoxyuridine; CFU;
Keywords: بیماری گرانولوماتوز مزمن; Database Analysis; GI; Intestine; Disease Phenotype; CGD; chronic granulomatous disease; GI; gastrointestinal; IBD; inflammatory bowel disease; NIH; National Institutes of Health; ROS; reactive oxygen species;
Keywords: بیماری گرانولوماتوز مزمن; Abscesos; adenitis; enfermedad granulomatosa crónica; granulomas; infecciones recurrentes; inmunodeficienciasAbscesses; Adenitis; Chronic Granulomatous Disease; Granulomas; Recurrent Infections; Immunodeficiency
Keywords: بیماری گرانولوماتوز مزمن; ALPS; Autoimmune lymphoproliferative syndrome; AT; Ataxia telangiectasia; CD; Complement deficiency; CGD; Chronic granulomatous disease; CHH; Cartilage-hair hypoplasia; CHS; Chediak-Higashi syndrome; CMC; Chronic mucocutaneous candidiasis; CN; Cyclic
Keywords: بیماری گرانولوماتوز مزمن; Immunology; primary immunodeficiency; dedicator of cytokinesis 8; HIV1; recombination-activating gene 1; intravenous immunoglobulin; common variable immunodeficiency; severe combined immunodeficiency; newborn screening; ADA; Adenosine deaminase; ApoE; Apo
Keywords: بیماری گرانولوماتوز مزمن; Primary immune deficiency; microscopy; cell biology; cytoskeleton; host defense; AP3; Adaptor protein 3; Arp2/3; Actin-related proteins 2 and 3; CDC42; Cell division cycle 42; CGD; Chronic granulomatous disease; CHS; Chediak-Higashi syndrome; CTL; Cytotox
Keywords: بیماری گرانولوماتوز مزمن; Pediatric lymphadenopathy; Cervical lymphadenopathy; Chronic granulomatous disease; Chédiak-Higashi syndrome; Cat-scratch disease;
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; Computed tomography; Bronchiectasis; Pulmonary nodules; Respiratory infections;
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; 123 dihydrorhodamine; Discoid lupus; Chronic granulomatous disease carriers
Keywords: بیماری گرانولوماتوز مزمن; BTK; Bruton tyrosine kinase; CGD; chronic granulomatous disease; CMC; chronic mucocutaneous candidiasis; γc; γ-common; HLH; hemophagocytic lymphohistiocytosis; HSCT; hematopoietic stem cell transplantation; ITK; IL2-inducible T cell kinase; NK; natural
Keywords: بیماری گرانولوماتوز مزمن; BAL; bronchoalveolar lavage; CFU; colony forming units; CGD; chronic granulomatous disease; ELA; neutrophil elastase; IA; invasive aspergillosis; NADPH; nicotinamide dinucleotide phosphate; NET; neutrophil extracellular trap; PMN; polymorphonuclear neutro
Keywords: بیماری گرانولوماتوز مزمن; NET; neutrophil extracellular trap; IDO; indoleamine 2,3-dioxygenase; CF; cystic fibrosis; CGD; chronic granulomatous disease; ROS; reactive oxygen species; RLU; relative luminescence unit; CFU; colony-forming unit; AhR; aryl hydrocarbon receptor; HRPO; h
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; Gene defects; NADPH oxidase; Immune defect; Inflammatory bowel disease;
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; dihydrorhodamine-1,2,3 assay; CYBB; CYBA; NCF1; NCF2; nicotinamide dinucleotide phosphate reduced oxidase; mean fluorescence intensity; stimulation index; AR; Autosomal recessive; A22R; A22 CGD with residual oxidase activity
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; Leukocyte adhesion deficiency; Severe congenital neutropenia; Neutrophils; Mouse models; Zebrafish models;
Keywords: بیماری گرانولوماتوز مزمن; Immunology; primary immunodeficiency; nuclear factor κB; autoimmunity; intravenous immunoglobulin; common variable immunodeficiency; severe combined immunodeficiency; newborn screening; gene therapy; ADA; Adenosine deaminase; ADAM; A disintegrin and meta
Successful transcatheter arterial antimicrobial and steroid therapy for refractory liver abscess in chronic granulomatous disease: A case report and review of literature
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; Liver abscess; Transcatheter arterial therapy;
How the phagocyte NADPH oxidase regulates innate immunity
Keywords: بیماری گرانولوماتوز مزمن; Reactive oxygen species; Chronic granulomatous disease; Autophagy; Inflammasome; Type 1 interferon;
Impaired X-CGD T cell compartment is gp91phox-NADPH oxidase independent
Keywords: بیماری گرانولوماتوز مزمن; CGD; Chronic Granulomatous Disease; NADPH; Nicotinammide adenina dinucleotide fosfato; TCR; T-cell reception; ROS; Reactive oxygen species; PBMC; Peripheral blood mononuclear cells; SIN-LVV; Self-inactivating lentiviral vector; CGD; T lymphocytes; TCRV-be
X-linked carriers of chronic granulomatous disease: Illness, lyonization, and stability
Keywords: بیماری گرانولوماتوز مزمن; Superoxide; X inactivation; dihydrorhodamine flow cytometry test; autoimmunity; lyonization; AIM; Autoimmune or inflammatory manifestation; CGD; Chronic granulomatous disease; DHR; Dihydrorhodamine 123; DLE; Discoid lupus erythematous; NADPH; Reduced nico
The proinflammatory effects of macrophage-derived NADPH oxidase function in autoimmune diabetes
Keywords: بیماری گرانولوماتوز مزمن; ABIS; All Babies in Southwest Sweden study; APC; Antigen presenting cells; Arg-1; Arginase 1; CB3; Coxsackievirus strain B3; CB4; Coxsackievirus strain B4; CGD; Chronic granulomatous disease; CSF-1; Colony-stimulating factor 1; AISY; Diabetes Autoimmunity
Conversion of NOX2 into a constitutive enzyme in vitro and in living cells, after its binding with a chimera of the regulatory subunits
Keywords: بیماری گرانولوماتوز مزمن; AA; all-cis-Arachidonic Acid; CCCP; carbonyl cyanide 3-chlorophenyl hydrazone; CGD; Chronic Granulomatous Disease; cyt c; cytochrome c; cyt b558; flavocytochrome b558; DPI; Diphenylene Iodonium; DISCO; Dichroism, Imaging and mass Spectrometry for Chemical
Polyamine- and NADPH-dependent generation of ROS during Helicobacter pylori infection: A blessing in disguise
Keywords: بیماری گرانولوماتوز مزمن; 8-OHdG; 8-hydroxy-2-deoxyguanosine; ABL1; ABL proto-oncogene 1; AhpC; alkyl hydroperoxide reductase; AKT1; V-Akt murine thymoma viral oncogene homolog 1; APEX1; endonuclease apurinic/apyrimidinic endodeoxyribonuclease 1; ARG1; arginase 1; ARG2; arginase 2
Down-regulation of NOX2 activity in phagocytes mediated by ATM-kinase dependent phosphorylation
Keywords: بیماری گرانولوماتوز مزمن; NOX; NADPH oxidase; ROS; reactive oxygen species; CGD; chronic granulomatous disease; PMA; Phorbol 12-myristate 13-acetate; fMLP; formyl-methionylleucyl-phenylalanine; DMF; dimethylformamide; DFP; diisopropylfluorophosphate; DPI; diphenylene iodonium; INT
A novel missense mutation in the NADPH binding domain of CYBB abolishes the NADPH oxidase activity in a male patient with increased susceptibility to infections
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; Immunodeficiency; Mycobacterium tuberculosis; Monocyte-derived macrophages;
Immune deficiencies, infection, and systemic immune disordersMycobacterial disease in patients with chronic granulomatous disease: AÂ retrospective analysis of 71 cases
Keywords: بیماری گرانولوماتوز مزمن; Mycobacteria; BCG; chronic granulomatous disease; tuberculosis; primary immunodeficiency; AR; Autosomal recessive; CGD; Chronic granulomatous disease; EM; Environmental mycobacteria; MSMD; Mendelian susceptibility to mycobacterial disease; NADPH; Nicotina
A founder effect for p47phoxTrp193Ter chronic granulomatous disease in Kavkazi Jews
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; NADPH oxidase; p47phox; NCF1; Kavkazi Jews; Founder effect
Defective B-cell proliferation and maintenance of long-term memory in patients with chronic granulomatous disease
Keywords: بیماری گرانولوماتوز مزمن; Chronic granulomatous disease; B cell; proliferation; long-term memory; measles; memory B-cell compartment; reactive oxygen species deficiency; Anti-Ig; F(abâ²)2 fragment goat anti-human IgA+IgG+IgM; ASC; Antibody-secreting cell; BCR; B-cell receptor; CG
Neutrophil NET formation is regulated from the inside by myeloperoxidase-processed reactive oxygen species
Keywords: بیماری گرانولوماتوز مزمن; CGD; chronic granulomatous disease; CL; chemiluminescence; DAG; sn-1,2-dioctanoylglycerol; DPI; diphenyleneiodonium; HRP; horseradish peroxidase; KRG; Krebs-Ringer phosphate buffer; MPO; myeloperoxidase; NETs; neutrophil extracellular traps; PEG; polyethy