Pathological cholesterol metabolism fails to modify electrophysiological properties of afflicted neurones in Niemann-Pick disease type C
Keywords: Niemann-Pick disease type C; neurones; electrophysiology; calcium homeostasis; cholesterol; ACSF; artificial cerebrospinal fluid; AP; action potential; (Ca2+)i; intracellular free calcium concentration; IPSPA; early inhibitory postsynaptic potentials; IPS