
The primary cause of muscle disfunction associated with substitutions E240K and R244G in tropomyosin is aberrant behavior of tropomyosin and response of actin and myosin during ATPase cycle
Keywords: 1،5-یادانس; Tropomyosin; F-actin; Myosin; Troponin; Ghost muscle fibres; Congenital myopathies; Fluorescence polarization; 1,5-IAEDANS; N-(iodoacetaminoethyl)-1-naphthyl-amine-5-sulfonic acid; 5-IAF; 5-iodoacetamidofluorescein; TM-WT; wild type recombinant Tpm1.1; TM