
Keywords: HD; Huntington disease; Htt; Huntingtin; MSN; medium spiny neuron; S1R; sigma-1 receptor; ER; endoplasmic reticulum; YAC128; yeast artificial chromosome 128Q expansion mice; 3-PPP; R(+)-3-(3-Hydroxyphenyl)-N-propylpiperidine hydrochloride; SOC; store-oper