Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; AP, alternative complement pathway; ELISA, enzyme-linked immunosorbent assay; ESRD, end-stage renal disease; CKD, chronic kidney disease; FB, factor B; FH, factor H; FI, factor I; MODS, multiple organ dysfunction
مقالات ISI aHUS، سندرم اورمیک همولیتیک آتیپیک (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; aPL, antiphospholipid; APLAS, antiphospholipid antibody syndrome; AT1-AA, agonistic autoantibodies to the angiotensin II type 1 receptor; CH50, complement hemolytic activity; C1-INH, C1 esterase inhibitor; CR1, co
C4b-binding protein: The good, the bad and the deadly. Novel functions of an old friend
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; C3b, activated complement factor 3; C4b, activated complement factor 4; C4BP, C4b-binding protein; CCP, complement control protein (domain); CRP, C-reactive protein; Gla, γ-carboxyglutamic acid; FH, factor H; FI,
The role of heparan sulfate as determining pathogenic factor in complement factor H-associated diseases
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; FH, complement factor H; HS, heparan sulfate; AP, alternative pathway; CCP, complement control protein domain; GAG, glycosaminoglycan; AMD, age-related macular degeneration; DDD, dense deposit disease; aHUS, atypical hemolytic uremic syndrome; dpX, degree
Functional characterization of two novel non-synonymous alterations in CD46 and a Q950H change in factor H found in atypical hemolytic uremic syndrome patients
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; HD, hemodialysis; CCP, complement control protein domain; CHO, Chinese hamster ovary cells; FBS, fetal bovine serum; HEK 293, human embryonic kidney 293 cells; NHS, normal human serum; PE, plasma exchange; PD, per
Anticomplement C5 therapy with eculizumab for the treatment of paroxysmal nocturnal hemoglobinuria and atypical hemolytic uremic syndrome
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; AE, adverse events; aHUS, atypical hemolytic uremic syndrome; AP, alternative pathway; C3bBb, C3 convertase; CKD, chronic kidney disease; CP, classical pathway; CR1, complement receptor 1; CD55, decay acceleration factor; DGKε, diacylglycerol kinase ε; FB
Novel insights in localization and expression levels of C5aR and C5L2 under native and post-transplant conditions in the kidney
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; ATN, acute tubular necrosis; C5aR, C5a receptor; C5L2, C5a like receptor 2; CNT, connecting tubule; DCT, distal convoluted tubule; aHUS, atypical hemolytic uremic syndrome; IF/TA, interstitial fibrosis and tubular atrophy; IL-6, interleukin-6; TAL, thick
Analysis of genetic and predisposing factors in Japanese patients with atypical hemolytic uremic syndrome
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; CFH, complement factor H; C3, complement component 3; MCP, membrane cofactor protein; CFI, complement factor I; CFB, complement factor B; CFD, complement factor D; THBD, thrombomodulin; CFHRs, CFH related genes; S
Role of complement and perspectives for intervention in transplantation
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; AAMR, acute antibody-mediated rejection; AMR, antibody-mediated rejection; aHUS, atypical hemolytic uremic syndrome; APCs, antigen-presenting cells; CsA, cyclosporine; CMR, cell-mediated rejection; CVF, cobra venom factor; C1-INH, C1 inhibitor; DSA, donor
CD46: The ‘multitasker’ of complement proteins
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; ADAM, a disintegrin and metalloproteinase; AP-1, activator protein 1; aHUS, atypical hemolytic uremic syndrome; AMD, age-related macular degeneration; Bcl-2, B-cell lymphoma 2; CCL, chemokine (C-C motif) ligand; CCP, complement control protein domain; CSL
Complement factor I in health and disease
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; C4BP, C4b-binding protein; CFI, complement factor I gene; CR1, complement receptor 1; DFP, diisopropylfluorophosphate; ESRD, end-stage renal disease; FH, Factor H; FI, Factor I; FIMAC, factor I membrane attack com
Inhibiting the C5–C5a receptor axis
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; CHIPS, chemotaxis inhibitory protein of Staphylococcus aureus; CFHR1, complement factor H-related protein 1; MAC, membrane attack complex; PNH, paroxysmal nocturnal hemoglobinuria; scFv, single-chain fragment vari
Complement deficiency states and associated infections
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; AMD, age-related macular degeneration; AP, alternative pathway; C1-INH, C1-inhibitor; C1qD, C1q deficiency; C2D, C2 deficiency; C3D, C3 deficiency; C4D, C4 deficiency; CFHR, complement factor H-related protein; CL
Complement control protein factor H: The good, the bad, and the inadequate
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; ARMD, age-related macular degeneration; DDD, dense deposit disease/membranoproliferative glomerulonephritis type II; fH-CR2, factor H-complement receptor 2 chimeric protein; AMBP-1, adrenomedullin binding protein-
The spectrum of phenotypes caused by variants in the CFH gene
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; AMD, age-related macular degeneration; AP, alternative pathway; BLD, basal laminar drusen; CCP, complement control protein; CFH, complement factor H; CFI, complement factor I; CRP, C-reactive protein; CR1, complem
A mutation in factor I that is associated with atypical hemolytic uremic syndrome does not affect the function of factor I in complement regulation
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; aHUS, atypical hemolytic uremic syndrome; C4BP, C4b-binding protein; CR1, complement receptor 1; FB, factor B; FH, factor H; FI, factor I; FIMAC, factor I membrane attack complex (domain); ESRD, end-stage renal disease; LDLr, low density lipoprotein recep
Implications of the initial mutations in membrane cofactor protein (MCP; CD46) leading to atypical hemolytic uremic syndrome
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; D+ HUS, diarrheal-associated hemolytic uremic syndrome; aHUS, atypical hemolytic uremic syndrome; MCP, CD46, membrane cofactor protein; CFH, complement factor H; MCP-HUS, MCP-associated HUS; CFH-HUS, CFH-associated HUS; IF-HUS, IF-associated HUS; RCA, reg
Insights into hemolytic uremic syndrome: Segregation of three independent predisposition factors in a large, multiple affected pedigree
Keywords: aHUS، سندرم اورمیک همولیتیک آتیپیک; MCP, membrane cofactor protein or CD46; aHUS, atypical hemolytic uremic syndrome; SNP, single nucleotide polymorphism; CFH, complement factor H; IF, factor IMembrane cofactor protein; Atypical hemolytic uremic syndrome; Complement factor I