Altered p53 and NOX1 activity cause bioenergetic defects in a SCA7 polyglutamine disease model
Keywords: اتاکسین -7; ATXN7; ataxin-7; ETC; electron transport chain; HD; Hungtinton's disease; NOX; Nadph oxidase; OxPhos; oxidative phosphorylation; PolyQ; polyglutamine; SCA7; spinocerebellar ataxia type 7; Neurodegeneration; NADPH oxidase; Oxidative phosphorylation; Metabo