Keywords: کمبود سیستم ایمنی متغیر; Hematopoietic stem cell transplantation; gammaretroviral vector; lentiviral vector; gene editing; site-specific endonuclease; zinc finger nuclease; CRISPR/Cas9; ADA-SCID; Adenosine deaminase-deficient severe combined immunodeficiency; CGD; Chronic granu
مقالات ISI کمبود سیستم ایمنی متغیر (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: کمبود سیستم ایمنی متغیر; Smith-Magenis syndrome; Chromosome 17p11.2 deletion; Immune deficiency; Autoantibody; TNFRSF13B; FLCN; TOM1L2; B-cell tolerance; BHDS; Birt-Hogg-Dubé syndrome; CVID; Common variable immune deficiency; EMR; Electronic medical records; FLCN; Folliculin; Hi
Keywords: کمبود سیستم ایمنی متغیر; Antibody deficiency; Asthma; Bronchiectasis; Chronic obstructive pulmonary disease; Chronic rhinosinusitis; Infection; ACOS; asthma-chronic obstructive pulmonary disease overlap syndrome; BODE; body-mass index, airflow obstruction, dyspnea, and exercise;
Keywords: کمبود سیستم ایمنی متغیر; Primary immunodeficiency; Adults; CGD; Chronic granulomatous disease; CVID; Common variable immune deficiency; HSCT; Hematopoietic stem cell transplant; IVIG; Intravenous immunoglobulin; PID; Primary immune deficiency;
Keywords: کمبود سیستم ایمنی متغیر; Bronchiectasis; Interstitial lung disease; Primary immunodeficiency disease; Common variable immune deficiency; Pulmonary complication;
Not All That Flattens Villi Is Celiac Disease: A Review of Enteropathies
Keywords: کمبود سیستم ایمنی متغیر; CD; celiac disease; CVID; common variable immune deficiency; HIV; human immunodeficiency virus;
Clonal and constricted T cell repertoire in Common Variable Immune Deficiency
Keywords: کمبود سیستم ایمنی متغیر; Common Variable Immune Deficiency; T cell receptor; High throughput sequencing; Junctional diversity; VDJ recombination; Clonality; Clone sharing; EBV; CMV; Adult;
Development and Initial Validation of a Questionnaire to Measure Health-Related Quality of Life of Adults with Common Variable Immune Deficiency: The CVID_QoL Questionnaire
Keywords: کمبود سیستم ایمنی متغیر; Burden of disease; Common variable immune deficiency; CVID_QoL; Disease-specific questionnaire; Quality of life; Questionnaire validation; BMI; Body mass index; CVID; Common variable immune deficiency; EF; Emotional functioning; EQ-5D; EuroQol-5 dimension
Atteinte des voies aériennes distales et immunodépression
Keywords: کمبود سیستم ایمنی متغیر; Greffe; Déficit immunitaire commun variable; Bronchiolite oblitérante; Granulomatose; Transplantation; Common variable immune deficiency; Bronchiolitis obliterans; Granulomatous disease;
Immune deficiencies, infection, and systemic immune disordersTNF receptor superfamily member 13b (TNFRSF13B) hemizygosity reveals transmembrane activator and CAML interactor haploinsufficiency at later stages of B-cell development
Keywords: کمبود سیستم ایمنی متغیر; TNFRSF13B; transmembrane activator and CAML interactor; B-cell tolerance; common variable immune deficiency; Smith-Magenis syndrome; ANA; Anti-nuclear antibody; APC; Allophycocyanin; APRIL; A proliferation-inducing ligand; BAFF; B-cell activation factor;
Malakoplakia and Primary Immunodeficiency
Keywords: کمبود سیستم ایمنی متغیر; CVID; Common variable immune deficiency; MG; Michaelis-Gutmann; SCID; Severe combined immunodeficiency; XLA; X-linked agammaglobulinemia;
Signal-peptide-peptidase-like 2a is required for CD74 intramembrane proteolysis in human B cells
Keywords: کمبود سیستم ایمنی متغیر; CMA; chromosomal microarray analysis; ICD; intracellular domain; MHCII; MHC class II complex; NTF; N-terminal fragment; RIP; regulated intramembrane proteolysis; SPP; Signal peptide peptidase; SPPL; Signal-peptide-peptidase-like; Invariant chain; CD74; B
B-lymphocyte lineage cells and the respiratory system
Keywords: کمبود سیستم ایمنی متغیر; B cells; plasma cells; plasmablasts; respiratory diseases; AID; Activation-induced cytidine deaminase; APRIL; A proliferation-inducing ligand; BAFF; B cell-activating factor of the TNF family; BAL; Bronchoalveolar lavage; BCMA; B-cell maturation antigen
Prevalence of prolonged and chronic poliovirus excretion among persons with primary immune deficiency disorders in Sri Lanka
Keywords: کمبود سیستم ایمنی متغیر; Primary immunodeficiency; Common variable immune deficiency; CVID; Vaccine derived polio virus; VDPV;
Adult Primary Immune Deficiency: What Are We Missing?
Keywords: کمبود سیستم ایمنی متغیر; Adult; Clinical; Common variable immune deficiency; Good's syndrome; Hypogammaglobulinemia; Immune deficiency; Primary immune deficiency; T-cell immune deficiency
Autoimmune manifestations in primary immune deficiencies
Keywords: کمبود سیستم ایمنی متغیر; Autoimmunity; Primary immune deficiency; Common variable immune deficiency; APECED; Complement
Granulomatous disease in common variable immunodeficiency
Keywords: کمبود سیستم ایمنی متغیر; Common variable immune deficiency; Granulomatous disease; Mortality; TNF-alpha; Lung disease; Autoimmunity
Transmembrane activator and calcium-modulating cyclophilin ligand interactor mutations in common variable immunodeficiency: Clinical and immunologic outcomes in heterozygotes
Keywords: کمبود سیستم ایمنی متغیر; Common variable immune deficiency; TACI; B cell; IgG; IgA; immune thrombocytopenia purpura; splenectomyAIHA, Autoimmune hemolytic anemia; APRIL, A proliferation inducing ligand; BAFF, B cell–activating factor; CFSE, Carboxyfluorescein succinimidyl ester;
Inflammatory and autoimmune complications of common variable immune deficiency
Keywords: کمبود سیستم ایمنی متغیر; Common variable immune deficiency; Autoimmunity; Idiopathic thrombocytopenia purpura; Hemolytic anemia