
Marked reduction of Na+, K+-ATPase and creatine kinase activities induced by acute lysine administration in glutaryl-CoA dehydrogenase deficient mice
Keywords: CK; creatine kinase; DCIP; dichloroindophenol; EDTA; ethylenediaminetetracetic acid; GA; glutaric acid; GA I; glutaric acidemia type I; GCDH; glutaryl-CoA dehydrogenase; Gcdhâ/â; glutaryl-CoA dehydrogenase deficient mice; 3HGA; 3-hydroxyglutaric acid;