
Altered sensitivity of cerebellar granule cells to glutamate receptor overactivation in the Cln3Δex7/8-knock-in mouse model of juvenile neuronal ceroid lipofuscinosis
Keywords: ACSF, artificial cerebrospinal fluid; AMPA, α-amino-3-hydroxy-5-methyl-4-isoxazolepropionate; CGC, cerebellar granule cell; Cln3-KO, Cln3-knock-out; CTZ, cyclothiazide; DIV, day in vitro; JNCL, juvenile neuronal ceroid lipofuscinoses; NMDA, N-methyl-d-asp