
DNA damage in Fabry patients: An investigation of oxidative damage and repair
Keywords: BER, base excision repair; DCF, dichlorofluorescein; DCFH, dihydrodichlorofluorescein; DI, damage index; EndoIII, endonuclease III; ERT, enzyme replacement therapy; FD, Fabry disease; FPG, formamidopyrimidine DNA-glycosylase; Gb3, globotriaosylceramideFab