Ivacaftor for the p.Ser549Arg (S549R) gating mutation - The Israeli experience
Keywords: Cystic fibrosis; Gating mutation; Ivacaftor; p.Ser549Arg (S549R); CF; Cystic Fibrosis; CFTR; Cystic fibrosis transmembrane conductance regulator; FEV1; forced expiratory volume in one second; FVC; functional vital capacity; FEF25-75%; mid forced expirator