دانلود مقالات ISI درباره GB3، globotriazylceramide + ترجمه فارسی

کاهش گلوکزیلکرامید در مدل ماوس بیماری فابری: اصلاح با استفاده از درمان جایگزینی آنزیم موفقیت آمیز

Reduced glucosylceramide in the mouse model of Fabry disease: Correction by successful enzyme replacement therapy

Keywords: GB3، globotriazylceramide; GlucCer, glucosylceramide; Cer, ceramide; ERT, Enzyme replacement therapy; Gb3, globotriaosylceramide; GSL, glycosphingolipid; LSD, lysosomal storage disease; Lyso-Gb3, globotriaosylsphingosineFabry disease; Enzyme replacement therapy; Ceramide; Glucosylc

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2014 سفارش ترجمه

Molecular and clinical studies in five index cases with novel mutations in the GLA gene

Keywords: GB3، globotriazylceramide; FD, Fabry disease; α-GAL A, α-galactosidase A; GB3, globotriaosylceramide; Lyso-GB3, globotriaosylsphingosine; GLA, GLA gene; ND, not determined; DGJ, 1-deoxygalactonojirimycin; ISE, intron splicing enhancerFabry disease; Alpha-galactosidase A; c.846_847d

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2016 سفارش ترجمه

Lysosome-associated protein 1 (LAMP-1) and Lysosome-associated protein 2 (LAMP-2) in a larger family carrier of Fabry disease

Keywords: GB3، globotriazylceramide; AUC, albumin/creatinine ratio; α–GAL, α-galactosidase A; ECC, echocardiogram; ECG, electrocardiogram; eGFR, glomerular filtration ratio; ERT, enzyme replacement therapy; FD, Fabry disease; Gb3, globotriaosylceramide; GLA, α-galactosidase A gene; LAMP-1, l

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2014 سفارش ترجمه

Invariant natural killer T cells are phenotypically and functionally altered in Fabry disease

Keywords: GB3، globotriazylceramide; iNKT, invariant natural killer T; α-GalCer, α-galactosylceramide; Gb3, globotriaosylceramide; ERT, enzyme replacement therapy; PMA, phorbol 12-myristate 13-acetate; TCR, T cell receptorLysosomal storage disorders; Fabry disease; Enzyme replacement therapy

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2013 سفارش ترجمه

Globotriaosylceramide is correlated with oxidative stress and inflammation in Fabry patients treated with enzyme replacement therapy

Keywords: GB3، globotriazylceramide; Cr, creatinine; CAT, catalase; Di-Tyr, di-tyrosine; FD, Fabry disease; FU, fluorescence units; Gb3, globotriaosylceramide; GLA, α-galactosidase A; GPx, glutathione peroxidase; GSH, reduced glutathione; H2O2, hydrogen peroxide; HPLC, high-performance liqui

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2012 سفارش ترجمه

An improved method for glycosaminoglycan analysis by LC–MS/MS of urine samples collected on filter paper

Keywords: GB3، globotriazylceramide; BMT, Bone marrow transplant; CHUS, Centre hospitalier universitaire de Sherbrooke; DS, Dermatan sulfate; ERT, Enzyme replacement therapy; ESI+, Electrospray ionization in positive ion mode; GAGs, Glycosaminoglycans; Gb3, Globotriaosylceramide; HS, Heparan

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2012 سفارش ترجمه

Reduction of elevated plasma globotriaosylsphingosine in patients with classic Fabry disease following enzyme replacement therapy

Keywords: GB3، globotriazylceramide; eNOS, endothelial nitric oxide synthase; ERT, enzyme replacement therapy; Gb2, galabiosylceramide; Gb3, globotriaosylceramide; GLA gene, α-galactosidase A gene; LVH, left ventricular hypertrophy; lysoGb3, globotriaosylsphingosine; OPA, o-phtaldialdehydeFa

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Binding, reconstitution and 2D crystallization of membrane or soluble proteins onto functionalised lipid layer observed in situ by reflected light microscopy

Keywords: GB3، globotriazylceramide; DDM, n-dodecyl-β-D-maltoside; DOPC, dioleoylphosphatidylcholine; DOTAP, 1,2-dioleoyl-3-trimethylammonium-propane; Ni++-NTA DOGS, 1,2-dioleoyl-sn-glycero-3-[(N-(5-amino-1-carboxypentyl) iminodiacetic acid)succinyl] (nickel salt); Gb3, globotriaosylceramide

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2011 سفارش ترجمه

Endocytosis and retrograde transport of Shiga toxin

Keywords: GB3، globotriazylceramide; Shiga toxin; Endocytosis; Gb3; Golgi; Glycosphingolipids; RicinER, endoplasmic reticulum; Gb3, globotriaosylceramide; SNX1, sorting nexin 1; SNX2, sorting nexin 2

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2010 سفارش ترجمه

Shiga toxin 1 interaction with enterocytes causes apical protein mistargeting through the depletion of intracellular galectin-3

Keywords: GB3، globotriazylceramide; Stx, Shiga toxin; Stx1B, B-subunit of Shiga toxin 1; EHEC, enterohemorrhagic Escherichia coli; Gb3, globotriaosylceramide; TNF-α, tumor necrosis factor α; CTB, B-subunit of cholera toxin; HRP, horse radish peroxidase; DPPIV, dipeptidylpeptidase IV; RT-PCR

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2010 سفارش ترجمه

Intracerebroventricular Shiga toxin 2 increases the expression of its receptor globotriaosylceramide and causes dendritic abnormalities

Keywords: GB3، globotriazylceramide; Gb3, Globotriaosylceramide; MAP2, Microtubule-associated protein 2; GFAP, Glial fibrillary acidic protein; Stx2, Shiga toxin 2Gb3; Shiga toxin 2; Neuronal damage; MAP2; GFAP; Intracerebroventricular

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2010 سفارش ترجمه

An easy and sensitive method for determination of globotriaosylceramide (Gb3) from urinary sediment: Utility for Fabry disease diagnosis and treatment monitoring

Keywords: GB3، globotriazylceramide; Gb3, globotriaosylceramide; α-Gal A, α-galactosidase A; ERT, enzyme replacement therapyFabry disease; Globotriaosylceramide; Urinary sediment; Diagnosis; Enzyme replacement therapy; Lysosomal storage disorders

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2009 سفارش ترجمه

Molecular cloning of apoptosis-inducing Pierisin-like proteins, from two species of white butterfly, Pieris melete and Aporia crataegi

Keywords: GB3، globotriazylceramide; Gb3, globotriaosylceramide; Gb4, globotetraosylceramideDNA ADP-ribosylation; Cytotoxicity; Apoptosis; Pierisin-3; Pierisin-4; DNA adducts; Oligo-capping method; TUNEL assay

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2009 سفارش ترجمه

The function of rhamnose-binding lectin in innate immunity by restricted binding to Gb3

Keywords: GB3، globotriazylceramide; BSA, bovine serum albumin; ConI, conger eel lectin I; CRD, carbohydrate recognition domain; CSL, chum salmon egg lectin; FAC, frontal affinity chromatography; HEPES, 2-[4-(hydroxyethyl)-1-piperazinyl] ethanesulfonic acid; Gb3, globotriaosylceramide; GEM,

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2009 سفارش ترجمه

Structural Basis of the Preferential Binding for Globo-Series Glycosphingolipids Displayed by Pseudomonas aeruginosa Lectin I

Keywords: GB3، globotriazylceramide; PA-IL, Pseudomonas aeruginosa lectin I; Gb3, globotriaosylceramide; Ka, association constant; TLC, thin-layer chromatography; MD, molecular dynamics; BL, Burkitt lymphoma; mAb, monoclonal antibody; LacCer, lactosylceramide; iGb3, isoglobotriaosylceramide;

دانلود رایگان متن کامل مقاله ISI 17 صفحه سال انتشار : 2008 سفارش ترجمه

Evidence for a role of glycosphingolipids in CXCR4-dependent cell migration

Keywords: GB3، globotriazylceramide; PPPP, DL-threo-1-phenyl-2-hexadecanoylamino-3-pyrrolidino-1-propanol; GCS, glucosylceramide synthase; GSL, glycosphingolipid; GlcCer, glucosylceramide; GalCer, galactosylceramide; LacCer, lactosylceramide; Gb3, globotriaosylceramide; C8-GlcCer, d-Glucosyl

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2007 سفارش ترجمه

The assembly of single domain antibodies into bispecific decavalent molecules

Keywords: GB3، globotriazylceramide; bsAb, bispecific antibody; gan, gene accession number; Gb3, globotriaosylceramide; KD, dissociation constant; sdAb, single domain antibody; VTB, verotoxin B subunit.Bispecific antibody; Decabody; Single domain antibody; Phage display

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2007 سفارش ترجمه

Alternate routes for drug delivery to the cell interior: Pathways to the Golgi apparatus and endoplasmic reticulum

Keywords: GB3، globotriazylceramide; APC, antigen presenting cells; CT, Cholera toxin; CTL, cytotoxic T lymphocytes; DT, Diphtheria toxin; HLE, E. coli heat labile toxin; ER, endoplasmic reticulum; ERAD, ER-associated protein degradation; GA, Golgi apparatus; Gb3, globotriaosylceramide; GFP,

دانلود رایگان متن کامل مقاله ISI 16 صفحه سال انتشار : 2007 سفارش ترجمه

Targeting antigens to dendritic cells in vivo

Keywords: GB3، globotriazylceramide; Adenovirus; Antigen; Cross-presentation; Dendritic cell; Liposome; TargetingCRD, carbohydrate-recognition domain; DC, dendritic cell; FcR, Fc receptor; Gb3, globotriaosylceramide; HSP, heat shock protein; Id, immunoglobulin idiotype; Ig, immunoglobulin; L

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2006 سفارش ترجمه

Sphingolipids of the nucleus and their role in nuclear signaling

Keywords: GB3، globotriazylceramide; CER, ceramide; CGN, cerebellar granule neurons; Ctx B, cholera toxin B subunit; DAG, diacylglycerol; ER, endoplasmic reticulum; Gb3, globotriaosylceramide; HRP, horseradish peroxidase; NCX, sodium calcium exchanger; NE, nuclear envelope; SM, sphingomyelin

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2006 سفارش ترجمه