C1 Inhibitor as a glycoprotein: The influence of polysaccharides on its function and autoantibody target
Keywords: HAE، آنژیوادم ارثی; AAE, acquired angioedema; C1Inh, C1 Inhibitor; C1Inh-HAE, hereditary angioedema with C1 Inhibitor deficiency; FXII, Factor XII; FXIIa, activated Factor XII; HAE, hereditary angioedema; HK, high-molecular-weight kininogenAcquired angioedema; C1 inhibitor;