Keywords: هموفیلی A; Haemophilia A; Haemophilia B; Prophylaxis; Factor VIII; Factor IX;
مقالات ISI هموفیلی A (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
A ROTEM method using APTT reagent and tissue factor as the clotting activators may better define bleeding heterogeneity in moderate or severe haemophilia A (part I: Study in plasma samples)
Keywords: هموفیلی A; Haemophilia A; Bleeding heterogeneity; ROTEM; Clotting activator; Coagulation profile;
Haemate P â zastosowanie w profilaktyce i leczeniu krwawieÅ w chorobie von Willebranda oraz indukcji immunotolerancji w hemofilii A powikÅanej inhibitorem
Keywords: هموفیلی A; Haemate P; choroba von Willebranda; hemofilia A; indukcja tolerancji immunologicznej; Haemate P; von Willebrand disease; Haemophilia A; Immune tolerance induction;
Supracondylar femoral osteotomy and knee joint replacement during the same surgical procedure in a type A haemophiliac patient with knee flexion deformity and ankylosis
Keywords: هموفیلی A; Osteotomy; Knee prosthesis; Haemophilia A; Ankylosis;
Haemophilia A and cardiovascular morbidity in a female SHAM syndrome carrier due to skewed X chromosome inactivation
Keywords: هموفیلی A; Moyamoya; Haemophilia A; Aortic coarctation; Hypertension; Arrhythmias; X chromosome inactivationSHAM, severe haemophilia A and moyamoya; F8, factor VIII gene; BRCC3, BRCA1/BRCA2-containing complex, subunit 3 gene; RT PCR, reverse transcription polymerase
Antibody profile in Indian severe haemophilia A patients with and without FVIII inhibitors
Keywords: هموفیلی A; Haemophilia A; FVIII; Inhibitors; Autoantibodies; India
Current view and outcome of ITI therapy - A change over time?
Keywords: هموفیلی A; aPCC; activated prothrombin complex concentrate; d; day; BU; Bethesda units; ED; exposure days; EHTSB; European Haemophilia Therapy Strategy Board; FVIII; factor eight; FIX; factor nine; HA; haemophilia A; HB; haemophilia B; IS; immunosuppression; I-ITI;
Is the cardiovascular toxicity of NSAIDS and COX-2 selective inhibitors underestimated in patients with haemophilia?
Keywords: هموفیلی A; Cardiovascular disease; Coxibs; Haemophilia A; Haemophilia B; NSAID;
Clinical use of Haemate® P in von Willebrand disease: A 25-year retrospective observational study
Keywords: هموفیلی A; Haemate; Humate; von Willebrand disease; Haemophilia A; von Willebrand factor; Factor VIII;
Development, upscaling and validation of the purification process for human-cl rhFVIII (Nuwiq®), a new generation recombinant factor VIII produced in a human cell-line
Keywords: هموفیلی A; Haemophilia A; Recombinant factor VIII; Human-cl rhFVIII; Nuwiq®; Purification process; Pathogen safety;
Regular ArticlePlasma concentration of protein Z and protein Z-dependent protease inhibitor in patients with haemophilia A
Keywords: هموفیلی A; Protein Z; protein Z-dependent protease inhibitor; haemophilia A; bleeding;
Characterisation of the post-translational modifications of a novel, human cell line-derived recombinant human factor VIII
Keywords: هموفیلی A; α-Gal; Galα1-3Galβ1-GlcNAc-R; Asn/N; asparagine; BHK; baby hamster kidney; CHO; Chinese hamster ovary; EIC; extracted ion chromatogram; FVIII; factor VIII; HA; Haemophilia A; HEK; human embryonic kidney; HexNAcHexNAc; hexosamine-hexosamine; HPAEC-PAD;
Seudotumor hemofílico: complicación poco frecuente en pacientes con deficiencia del factor VIII y IX que asemeja sarcoma de partes blandas
Keywords: هموفیلی A; Seudotumor hemofílico; Hemofilia A; TratamientoHaemophilic pseudotumour; Haemophilia A; Treatment
Haemophilia A patients are not at increased risk of hepatitis A virus infection: An Egyptian experience
Keywords: هموفیلی A; Hepatitis A virus; Haemophilia A; Hepatitis A vaccine
Les anticorps anti-FVIII et anti-FIX
Keywords: هموفیلی A; Hémophilie A; hémophilie B; inhibiteurs; coagulation; réponse immunitaire; facteur VIII; facteur IX; Haemophilia A; haemophilia B; inhibitors; coagulation; immune response; factor III; factor IX;
Laboratory identification of factor inhibitors: an update
Keywords: هموفیلی A; APTT; Bethesda assay; Factor inhibitors; lupus inhibitor; mixing tests; replacement therapy; APTT; activated partial thromboplastin time; aVWS; acquired von Willebrand syndrome; DIC; disseminated intravascular coagulation; dRVVT; dilute Russell's viper
Clinical efficacy of a novel VWF-containing FVIII concentrate, Wilate®, in the prophylaxis and treatment of bleeding episodes in previously treated haemophilia A patients
Keywords: هموفیلی A; Haemophilia A; factor VIII; haemostatic efficacy; surgery; previously treated patients; Wilate®;
Prophylactic therapy in haemophilia
Keywords: هموفیلی A; Haemophilia A; Haemophilia B; Factor VIII; Factor IX
Molecular pathology of haemophilia A in Indian patients: Identification of 11 novel mutations
Keywords: هموفیلی A; Haemophilia A; Factor VIII mutations; Conformation sensitive gel electrophoresis; Genetic diagnosis
The role of VWF for the success of immune tolerance induction
Keywords: هموفیلی A; FVIII inhibitors; Factor VIII (FVIII); Haemophilia A; Immune tolerance induction (ITI); von Willebrand factor (VWF)
von Willebrand factor and transforming growth factor-beta modulate immune response against coagulation factor VIII in FVIII-deficient mice
Keywords: هموفیلی A; Haemophilia A; Factor VIII; Factor VIII antibody; Transforming growth factor β; von Willebrand factor
Management of factor VIII inhibitors
Keywords: هموفیلی A; haemophilia A; immune tolerance; inhibitors; prothrombin complex concentrates; recombinant factor VIIa
Hipertrofia muscular en sujetos hemofÃlicos tras estimulación eléctrica muscular
Keywords: هموفیلی A; Hemofilia A; Estimulación eléctrica muscular; Hipertrofia; Quadriceps femoris; Haemophilia A; Muscular electrical stimulation; Hypertrophy; Quadriceps femoris;