Keywords: پروتئین huntingtin; Huntington disease; Huntingtin; Calpains; Calpastatin; Proteolytic cleavage; Aggregation; CAPN; calpain; CAST; calpastatin protein; Cast; mouse calpastatin gene; HD; Huntington disease; HDKI; HdhQ111 knock-in mice; Htt; huntingtin protein; polyQ; polyglut
مقالات ISI پروتئین huntingtin (ترجمه نشده)
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Keywords: پروتئین huntingtin; BACHD; bacterial artificial chromosome mouse model of HD; HD; Huntington's disease; HTT; Huntingtin protein; Htt; huntingtin gene; ipRGCs; intrinsically photoreceptive retinal ganglion cells; KI; knock in; SCN; suprachiasmatic nucleus; UCLA; University of
Keywords: پروتئین huntingtin; HD; Huntington's disease; PolyQ; polyglutamine; FRET; fluorescence resonance energy transfer; Htt; huntingtin protein; CD; circular dichroism; FTIR; Fourier transform infrared spectroscopy; XRD; X-ray diffraction; NMR; nuclear magnetic resonance; AFM; ato
Keywords: پروتئین huntingtin; Dendritic spine; Synaptic plasticity; Neurodegenerative diseases; Psychiatric disorders; Glutamate receptor; Calcium signaling; ADHD; attention deficit hypersensitive disorders; FXS; Fragile X-syndrome; CNS; central nervous system; GABA; gamma amino butyr
Intravenous immunoglobulin ameliorates motor and cognitive deficits and neuropathology in R6/2 mouse model of Huntington's disease by decreasing mutant huntingtin protein level and normalizing NF-κB signaling pathway
Keywords: پروتئین huntingtin; Huntington's disease; Polyglutamine; Intravenous immunoglobulin; Huntingtin protein;
Synaptopathic mechanisms of neurodegeneration and dementia: Insights from Huntington's disease
Keywords: پروتئین huntingtin; 5-HT; 5-hydroxytryptamine; 7,8-DHF; 7,8-dihydroxyflavone; ACh; acetylcholine; AD; adenosine; ADL; activities of daily living; AMPA; α-amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid; AMPK; 5â²AMP-activated protein kinase; BDNF; brain-derived neurotro
Differential recruitment of UBQLN2 to nuclear inclusions in the polyglutamine diseases HD and SCA3
Keywords: پروتئین huntingtin; polyQ; polyglutamine; HD; Huntington's disease; HTT; Huntingtin protein; SCA3; spinocerebellar ataxia type 3; UPP; ubiquitin-proteasome pathway; UBL; ubiquitin-like domain; UBA; ubiquitin-associated domain; PLIC-1; integrin-associated protein and cytosk
A plant cell model of polyglutamine aggregation: Identification and characterisation of macromolecular and small-molecule anti-protein aggregation activity in vivo
Keywords: پروتئین huntingtin; Huntingtin protein; Protein aggregation; PolyQ; LEA protein; sHSP protein; EGCG;
Altered selenium status in Huntington's disease: Neuroprotection by selenite in the N171-82Q mouse model
Keywords: پروتئین huntingtin; HD; Huntington's disease; htt; huntingtin protein; mhtt; mutant huntingtin protein; FRET; Förster resonance energy transfer; DARPP32; Dopamine and cyclic AMP-regulated phosphoprotein; GSH; glutathione; GSSG; oxidized glutathione; AD; Alzheimer's disease;
Inactivation of Apaf1 reduces the formation of mutant huntingtin-dependent aggregates and cell death
Keywords: پروتئین huntingtin; AkoMEFS; Apaf1 knock-out mice; Apaf1; apoptotic protease-activating factor 1; Cyt c; cytochrome c; DMEM; Dulbecco's Modified Eagle Medium; DOXO; doxorubicin; DTT; dithiothreitol; EDTA; ethylenediaminetetraacetic acid; EGFP; enhanced green fluorescent pr
Autophagy, polyphenols and healthy ageing
Keywords: پروتئین huntingtin; AD; Alzheimer's disease; AMP; adenosine monophosphate; AMPK; adenosine monophosphate activated protein kinase; APP; amyloid beta precursor protein; Atg; autophagy (related gene); ATP; adenosine triphosphate; AV; autophagic vacuoles; Aβ; amyloid beta; Bcl
Examination of mesenchymal stem cell-mediated RNAi transfer to Huntington's disease affected neuronal cells for reduction of huntingtin
Keywords: پروتئین huntingtin; MSC; Mesenchymal stem cells; HD; Huntington's disease; HTT; huntingtin protein; HTT142; huntingtin fragment containing exon 1 and containing approximately 100 CAG repeats; U87; glioblastoma cell line; SH-SY5Y; neuroblastoma cell line; GFP; enhanced green
Engineered antibody therapies to counteract mutant huntingtin and related toxic intracellular proteins
Keywords: پروتئین huntingtin; BBB; blood-brain barrier; dAbs; domain antibodies; HD; Huntington's disease; HSC70; heat shock cognate protein 70; HSP70; heat shock protein 70; HTT; huntingtin protein; mHTT; mutant huntingtin protein; PEST; Proline (P), Glutamic Acid (E), Serine (S) a
Characterization of cDNA encoding a human sperm membrane protein sharing homology with Huntingtin protein
Keywords: پروتئین huntingtin; FASA-57; Huntingtin protein; Testis; Spermatozoa;
Neuronal intranuclear inclusions and neuropil aggregates in HdhCAG(150) knockin mice
Keywords: پروتئین huntingtin; Huntington disease; polyglutamine; neurodegeneration; ataxia; striatum; CBP; cyclic AMP response element binding protein; DAB; diaminobenzidine; DARPP-32; dopamine and cyclic AMP regulated phosphoprotein-23 kDa; HD; Huntington disease; htt; Huntingtin pro