Keywords: ایده بیون; Retinopathy; Optic neuropathy; Age-related macular degeneration; Diabetic retinopathy; Glaucoma; Leber's hereditary optic neuropathy (LHON); Mitochondrial dysfunction; CoQ10; Idebenone; EPI-743; MitoQ; SkQ1; Ocluvia; MTP-131;
مقالات ISI ایده بیون (ترجمه نشده)
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Keywords: ایده بیون; Inflammatory pain; Oxidative stress; Antioxidant; Idebenone; HP-β-cyclodextrins;
Keywords: ایده بیون; Idebenone; Membranes; 2H NMR; 1H NOESY MAS-NMR; DSC; WAXD; SAXD
Keywords: ایده بیون; Duchenne muscular dystrophy; Idebenone; Respiratory function; Airway infection;
Keywords: ایده بیون; Idebenone; Differential scanning calorimetry; Solid lipid nanoparticles; Surfactants;
Keywords: ایده بیون; Idebenone; Multiple sclerosis; Oxidative stress; EAE; Inflammation;
The idebenone metabolite QS10 restores electron transfer in complex I and coenzyme Q defects
Keywords: ایده بیون; CoQ; coenzyme Q; CRC; Ca2+ retention capacity; FCCP; carbonylcyanide-p-trifluoromethoxyphenyl hydrazone; Cs; cyclosporin; DMEM; Dulbecco's modified Eagle's medium; hpf; hours post-fertilization; idebenone; 2-(10-hydroxydecyl)-5,6-dimethoxy-3-methyl-cycloh
Idebenone is a cytoprotective insulin sensitizer whose mechanism is Shc inhibition
Keywords: ایده بیون; Idebenone (PubChem CID: 3686); acarbose (PubChem CID: 41774); BI78D3 (PubChem CID: 2747117); candesartan cilexetil (PubChem CID: 2540); PQ401 (PubChem CID: 9549305); Src I1 (PubChem CID: 1474853); 17a-Hydroxyprogesterone (PubChem CID: 6238); FPA 124 (PubC
Efficient attenuation of Friedreich's ataxia (FRDA) cardiomyopathy by modulation of iron homeostasis-human induced pluripotent stem cell (hiPSC) as a drug screening platform for FRDA
Keywords: ایده بیون; Friedreich's ataxia; Induced pluripotent stem cells; Cardiomyopathy; Idebenone; Deferiprone;
Border between natural product and drug: Comparison of the related benzoquinones idebenone and coenzyme Q10
Keywords: ایده بیون; Benzoquinone; Idebenone; Coenzyme Q10; Mitochondria; AntioxidantCoQ, coenzyme Q; DMD, Duchene Muscular Dystrophy; ETC, electron transport chain; NQO1, NAD(P)H-quinone oxidoreductase 1; ROS, reactive oxygen species
Idebenone protects against oxidized low density lipoprotein induced mitochondrial dysfunction in vascular endothelial cells via GSK3β/β-catenin signalling pathways
Keywords: ایده بیون; Idebenone; oxLDL; Apoptosis; Mitochondria; GSK3β/β-catenin signallingpathways;
Administration of CoQ10 analogue ameliorates dysfunction of the mitochondrial respiratory chain in a mouse model of Angelman syndrome
Keywords: ایده بیون; Neurodegenerative disorder; Angelman syndrome; Mitochondrial respiratory chain; Coenzyme Q10 analogue; Idebenone; Cytochrome oxidase subunit IV; Glutathione disulfide;
Novel aberrant genetic and epigenetic events in Friedreich׳s ataxia
Keywords: ایده بیون; FRDA; Friedreich׳s ataxia; FXN; frataxin; ISC; iron-sulphur cluster; hPDL; human periodontal ligament; CASP3; active caspase-3; DNMT; DNA methyltransferase; CpG; cytosine phosphate group guanine; TSS; transcription start site; UP; upstream GAA repetiti
Single-step synthesis of idebenone from Coenzyme Q0 via free-radical alkylation under silver catalysis
Keywords: ایده بیون; Idebenone; Decarboxylative cross-coupling; C-H activation; Free-radical alkylation;
Coenzyme Q10 as a therapy for mitochondrial disease
Keywords: ایده بیون; Coenzyme Q10; Mitochondrial respiratory chain; Idebenone; EPI-743; Oxidative stress
Idebenone-loaded solid lipid nanoparticles for drug delivery to the skin: In vitro evaluation
Keywords: ایده بیون; Idebenone; Skin permeation; Skin penetration; Solid lipid nanoparticles; Skin delivery;
Crystallization of an active pharmaceutical ingredient that oils out
Keywords: ایده بیون; Idebenone; Oiling out; Crystallization; Purification
The effects of idebenone on mitochondrial bioenergetics
Keywords: ایده بیون; CRC; calcium retention capacity; Cs; cyclosporin; DMEM; Dulbecco's modified Eagle's medium; ÎÏm; mitochondrial membrane potential difference; DTT; dithiothreitol; FCCP; carbonylcyanide-p-trifluoromethoxyphenyl hydrazone; LHON; Leber's hereditary optic n
Therapies in inborn errors of oxidative metabolism
Keywords: ایده بیون; mitochondrial therapy; clinical trials; idebenone; MNGIE
Analysis of the structural and mechanistic factors in antioxidants that preserve mitochondrial function and confer cytoprotection
Keywords: ایده بیون; Idebenone; Mitochondrial dysfunction; Reactive oxygen species; Electron transport chain
Leber hereditary optic neuropathy – Therapeutic challenges and early promise
Keywords: ایده بیون; gene therapy; idebenone; Leber hereditary optic neuropathy; LHON; mitochondrial DNA; optic atrophy
Effect of long-term oral treatment with L-arginine and idebenone on the prevention of stroke-like episodes in an adult MELAS patient
Keywords: ایده بیون; MELAS syndrome; L-arginine; Idebenone; Stroke-like episodes; Syndrome de MELAS; L-arginine; Idebenone; Ãpisodes pseudovasculaires;
Idebenone as a novel, therapeutic approach for Duchenne muscular dystrophy: Results from a 12 month, double-blind, randomized placebo-controlled trial
Keywords: ایده بیون; Duchenne; Muscular dystrophy; Treatment; Idebenone; Cardiac; Cardiomyopathy; Respiratory function
Nitric oxide pros and cons: The role of l-arginine, a nitric oxide precursor, and idebenone, a coenzyme-Q analogue in ameliorating cerebral hypoxia in rat
Keywords: ایده بیون; Nitric oxide; Hypoxia; ROS; l-Arginine; Idebenone; ATP; Antioxidant
Antioxidant idebenone-loaded nanoparticles based on chitosan and N-carboxymethylchitosan
Keywords: ایده بیون; Antioxidant; Idebenone; Nanoparticles; Chitosan; N-Carboxymethylchitosan; Spray-dryer; Stability; Mucous membrane irritation
Treatment of mitochondrial electron transport chain disorders: A review of clinical trials over the past decade
Keywords: ایده بیون; Controlled clinical trials; Mitochondrial disorders; Dichloroacetate; Arginine; Coenzyme Q10; Idebenone; Parkinson disease; Friedreich ataxia; Exercise;
Inhibition of glycerophosphate-dependent H2O2 generation in brown fat mitochondria by idebenone
Keywords: ایده بیون; Mitochondrial glycerophosphate dehydrogenase; Succinate dehydrogenase; Reactive oxygen species; Idebenone; Coenzyme Q analogs
A calorimetric evaluation of the interaction of amphiphilic prodrugs of idebenone with a biomembrane model
Keywords: ایده بیون; Idebenone; Lipoamino acids; Lipophilicity; Amphiphilicity; DSC; Biomembrane model