
Defective cellular trafficking of the bone morphogenetic protein receptor type II by mutations underlying familial pulmonary arterial hypertension
Keywords: TGF-β, transforming growth factor beta; SMAD, small mothers against decapentaplegic; Ig, immunoglobulin(s); BSA, bovine serum albumin; FITC, fluorescein-isothiocyanate; TRITC, tetramethylrhodamine-isothiocyanate; SDS, sodium dodecyl sulfate; PAGE, polyacr