دانلود مقالات ISI درباره Isovaleryl-Coa Dehydrogenase + ترجمه فارسی

Kinetic and spectral properties of isovaleryl-CoA dehydrogenase and interaction with ligands

Keywords: Acyl-CoA dehydrogenase; Electron-transferring flavoprotein; ACADs; acyl-CoA dehydrogenases; BCAD; butyryl-CoA dehydrogenase; DCIP; dichlorophenylindolphenol; ETF; electron transfer flavoprotein; CTC; charge transfer complex; IBD; isobutyryl-CoA dehydrogen

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2015 سفارش ترجمه

Identification of a novel IVD mutation in a consanguineous family with isovaleric acidemia

Keywords: IVD; Isovaleryl-CoA dehydrogenase; IV; Isovaleryl-CoA dehydrogenase gene; IVA; Isovaleric academia; MS; Mass spectrometry, tandem mass spectrometry; NBSPs; Newborn screening programs; GCMS; Gas chromatography-mass spectrometry; MRI; Magnetic resonance i

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2013 سفارش ترجمه

Clinical and molecular analysis of isovaleric acidemia patients in the United Arab Emirates reveals remarkable phenotypes and four novel mutations in the IVD gene

Keywords: Isovaleric acidemia; Isovaleryl-CoA dehydrogenase; IVA; IVD

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2012 سفارش ترجمه

Alteration of mitochondrial protein complexes in relation to metabolic regulation under short-term oxidative stress in Arabidopsis seedlings

Keywords: Arabidopsis thaliana; Mitochondria; Oxidative stress; Blue native/SDS-PAGE; Protein complex; Metabolite profiling; Tricarboxylic acid cycle; Glycolysis; Ascorbate; Amino acid metabolism; 2D; two dimensional; AlaAT; alanine aminotransferase; BN; blue-nat

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2011 سفارش ترجمه

2-Methylbutyryl-coenzyme A dehydrogenase deficiency: Functional and molecular studies on a defect in isoleucine catabolism

Keywords: 2-Methylbutyryl-CoA dehydrogenase; Methylbutyrylglycinuria; Isovaleryl-CoA dehydrogenase; Isovaleric acidemia; Organic acids; Newborn screening; Acylcarnitines; Valproic acid; Branched-chain amino acids; Fibroblasts

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2008 سفارش ترجمه

Separation and identification of plasma short-chain acylcarnitine isomers by HPLC/MS/MS for the differential diagnosis of fatty acid oxidation defects and organic acidemias

Keywords: Acylcarnitine isomers; Tandem mass spectrometry; Fatty acid oxidation defects; Isovaleryl-CoA dehydrogenase; 3-Methylcrotonyl-CoA carboxylase; β-Ketothiolase; 3-Hydroxy-3-methylglutaryl-CoA lyase; Pivaloylcarnitine

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2007 سفارش ترجمه

Different spectrum of mutations of isovaleryl-CoA dehydrogenase (IVD) gene in Korean patients with isovaleric acidemia

Keywords: Isovaleric acidemia; IVD; Isovaleryl-CoA dehydrogenase; Acyl-CoA dehydrogenase; Mutation; Korean

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2007 سفارش ترجمه

Functional analysis of acyl-CoA dehydrogenase catalytic residue mutants using surface plasmon resonance and circular dichroism

Keywords: Isovaleryl-CoA dehydrogenase; Short-chain acyl-CoA dehydrogenase; Electron-transferring flavoprotein; Surface plasmon resonance; Circular dichroism

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2006 سفارش ترجمه

Establishment of a practical enzymatic assay method for determination of isovaleryl-CoA dehydrogenase activity using high-performance liquid chromatography

Keywords: Isovaleryl-CoA dehydrogenase; Enzyme assay; 3-Methylcrotonyl-CoA; High-performance liquid chromatography;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2005 سفارش ترجمه