Keywords: AC; Amsterdam criteria; AFAP; attenuated familial adenomatous polyposis; APC; adenomatous polyposis coli; CAP; College of American Pathologists; CD; Crohn disease; CLIA; Clinical Laboratory Improvement Amendments; CRC; colorectal cancer; dMMR; deficient m
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Keywords: cholestasis; biliary cirrhosis; MDR3; immunostaining;
Keywords: Hepatocellular carcinoma; ICG; Transporter; MDR3; OATP1B3;
Keywords: PBC; primary biliary cirrhosis; CMVs; canalicular membrane vesicles; mAb1F9; monoclonal antibody 1F9; mAb1F9-Ag; mAb1F9 antigen; UDCA; ursodeoxycholic acid; MALDI-TOF/TOF; matrix assisted laser desorption/ionization-tandem time-of-flight analysis; MS; mas
Reduced Hepatocellular Expression of Canalicular Transport Proteins in Infants with Neonatal Cholestasis and Congenital Hypopituitarism
Keywords: cholestasis; congenital hypopituitarism; septo-optic dysplasia; canalicular ectoenzymes; canalicular transport proteins; ACTH; Adrenocorticotropic hormone; BSEP; Bile salt export pump; CD13; Alanyl aminopeptidase; FIC1; Familial intrahepatic cholestasis t
Bile acid receptors in the biliary tree: TGR5 in physiology and disease
Keywords: AC; adenylate cyclase; BS; bile salt; BSEP; bile salt export pump (ABCB11); CA; cholic acid/cholate; cAMP; cyclic AMP; CBDL; common bile duct ligation; CCA; cholangiocarcinoma; CDCA; chenodeoxycholic acid/chenodeoxycholate; CD95L; CD95 ligand; CFTR; cysti
Post-transplant cholangiopathy: Classification, pathogenesis, and preventive strategies
Keywords: AE2; Anion exchanger 2 (cholangiocyte Clâ/HCO3â transporter); ATP; Adenosine triphosphate; BSEP; Bile salt export pump; CFTR; Cystic fibrosis transmembrane conductance regulator; CIT; Cold ischemia time; CMV; Cytomegalovirus; DBD; Donation after brain
Natural products as modulators of the nuclear receptors and metabolic sensors LXR, FXR and RXR
Keywords: Natural products; Nuclear receptors; Liver X receptor; Farnesoid X receptor; Retinoid X receptor; Metabolic syndrome; Precision medicine; 6-ECDCA; 6α-ethyl-chenodeoxycholic acid (obeticholic acid); AA; arachidonic acid; ABC; ATP-binding cassette transpor
8-Methoxypsoralen disrupts MDR3-mediated phospholipids efflux and bile acid homeostasis and its relevance to hepatotoxicity
Keywords: MDR3; multidrug resistance 3 P glycoprotein; 8-MOP; 8-methoxypsoralen; SD; Sprague-Dawley; PC; phosphatidylcholine; PUVA; psoralens plus UVA therapy; ALT; alanine-aminotransferase; AST; aspartate-aminotransferase; ABC; ATP-binding cassette; PFIC3; progres
Comparison of in silico prediction and experimental assessment of ABCB4 variants identified in patients with biliary diseases
Keywords: ATP; Adenosine triphosphate; ABC; ATP-binding cassette; ICP; Intrahepatic cholestasis of pregnancy; LPAC; Low phospholipid-associated cholelithiasis; NBD; Nucleotide-binding domain; PFIC3; Progressive familial intrahepatic cholestasis type 3; Cholestasis;
Sequencing of FIC1, BSEP and MDR3 in a large cohort of patients with cholestasis revealed a high number of different genetic variants
Keywords: FIC1; BSEP; MDR3; ATP8B1; ABCB11; ABCB4; ICP; LPAC; BRIC; PFIC; SNP;
Oleanolic acid attenuates obstructive cholestasis in bile duct-ligated mice, possibly via activation of NRF2-MRPs and FXR antagonism
Keywords: OA; oleanolic acid; LCA; lithocholic acid; UDCA; ursodeoxycholic acid; PBC; primary biliary cirrhosis; PSC; primary sclerosing cholangitis; MRP; multidrug resistance-associated protein; NRF2; nuclear factor-E2-related factor; siRNA; small interfering RNA;
Expression of MDR1 and MDR3 gene products in paclitaxel-, doxorubicin- and vincristine-resistant cell lines
Keywords: Drug-resistant cancer; Drug transporters; Expression levels; MDR3
Functional characterization of genetic variations in the MDR3 promoter
Keywords: MDR3; Promoter; Haplotype; NF-Y; Polymorphism; Transcription;
The histidin-loop is essential for transport activity of human MDR3. A novel mutation of MDR3 in a patient with progressive familial intrahepatic cholestasis type 3
Keywords: MDR3; multi drug resistance protein 3; PFIC; progressive familial intrahepatic cholestasis; GGT; gamma-glutamyltransferase; WBC; white blood cell Count; HAV; HBV, and HCV, Hepatitis A, B and C; TSH; thyroid stimulating hormon; BSEP; bile salt export pump;
A new splicing site mutation of the ABCB4 gene in intrahepatic cholestasis of pregnancy with raised serum γ-GT
Keywords: ABCB4; γ-GT; Intrahepatic cholestasis of pregnancy; MDR3; mRNA analysis; Splicing mutation
Altered bile composition after liver transplantation is associated with the development of nonanastomotic biliary strictures
Keywords: ALP; alkaline phosphatase; ALT; alanine aminotransferase; AST; aspartate aminotransferase; ASBT; apical sodium-dependent bile acid transporter; AUC; area under the curve; BS; bile salts; BSEP; bile salt export pump; CH; cholesterol; FI; fold induction; γ
Genetic factors of susceptibility and of severity in primary biliary cirrhosis
Keywords: PBC; primary biliary cirrhosis; CTLA-4; cytotoxic T-lymphocyte antigen 4; TNFα; tumor necrosis factor α; SNP; single nucleotide polymorphism; Ht SNP; haplotype-tagging single nucleotide polymorphism; MDR1; multidrug resistance 1; UDCA; ursodeoxycholic a
Diagnosis and Management of Cholestatic Liver Disease
Keywords: AMA; antimitochondrial antibodies; BSEP; bile salt export pump; CFTR; cystic fibrosis transmembrane regulator; ERCP; endoscopic retrograde cholangiopancreatography; GGT; γ-glutamyltranspeptidase; ICP; intrahepatic cholestasis of pregnancy; MDR3; human mu
Liver diseases unique to pregnancy
Keywords: Pregnancy; Liver; Hyperemesis gravidarum; Vomiting; Dehydration; Weight loss; Intrahepatic; Cholestasis; Cholestatic; Bile acids; MDR3; ABCB4; Itching; Pruritus; Icterus; ALT; AST; Cholestyramine; Ursodeoxycholic acid; Vitamin K; Antipruritics; Preeclamps
Developmental expression of canalicular transporter genes in human liver
Keywords: Cholestasis; BSEP; MDR3; MRP2; Ontogeny;