
Disturbance in Z-Disk Mechanosensitive Proteins Induced by a Persistent Mutant Myopalladin Causes Familial Restrictive Cardiomyopathy
Keywords: CARP/ANKRD1; ERK1/2; fibrosis; remodelingCARP/ANKRD1, cardiac ankyrin repeat protein; DES, desmin; ERK, extracellular signal–regulated kinase; FRCM, familial restrictive cardiomyopathy; HF, heart failure; LV, left ventricular; MLP, muscle LIM protein; MYP