Characterization of the MPS I-H knock-in mouse reveals increased femoral biomechanical integrity with compromised material strength and altered bone geometry
Keywords: MPS I, mucopolysaccharidosis type I; IDUA, α-L-iduronidase; GAGs, glycosaminoglycans; μCT, microcomputed tomography; BMDD, bone mineral density distribution; FWHM, full width at half maximum; BV/TV, bone volume/total volume; SMI, structure model index; Tm