
Species-specific differences in the processing of acid α-glucosidase are due to the amino acid identity at position 201
Keywords: GAA, acid α-glucosidase; rhGAA, recombinant human acid α-glucosidase; CHO, Chinese hamster ovary; MSX, methionine sulfoximine; ERT, enzyme replacement therapyAcid α-glucosidase; Glycogen storage disease type II; Pompe disease; Lysosome processing