RPTPζ/phosphacan is abnormally glycosylated in a model of muscle-eye-brain disease lacking functional POMGnT1
Keywords: عضله چشم مغز بیماری; α-DG; α-dystroglycan; chABC; chondroitinase ABC; CMDs; congenital muscular dystrophies; CNS; central nervous system; CP; cortical plate; CS-GAG; chondroitin sulfate glycosaminoglycan; E; embryonic day; ECM; extracellular matrix; EDTA; ethylenediamminete