
Keywords: AGU; aspartylglucosaminuria; GA; glycosylasparaginase; NAcGlc-Asn; N4-(β-N-acetylglucosaminyl)-l-asparagine; Ntn; N-terminal nucleophile; β-AHA; l-aspartic acid β-hydroxamate; Asp(pNA)-OH; aspartic acid β-(p-nitroanilide); r.m.s.d.; root mean square d