Early effect of NTBC on renal tubular dysfunction in hereditary tyrosinemia type 1
Keywords: P، فسفات; HT1, hereditary tyrosinemia type 1; FAA, fumarylacetoacetate; MAA, maleylacetoacetate; SA, succinylacetone; SAA, succinylacetoacetate; NTBC, 2-(2nitro-4-trifluoromethylbenzoyol)-1,3 cyclohexanedione nitisinone; P, phosphate; TRP, tubular reabsorption of p