
Keywords: PDH، پیرووات دهیدروژناز; DHTKD1, dehydrogenase E1 and transketolase domain containing 1; H2O2, hydrogen peroxide; OA, 2-oxoadipate; OADH, 2-oxoadipate dehydrogenase; OGDH, 2-oxoglutarate dehydrogenase; PDH, pyruvate dehydrogenase; BCOAD, branched chain 2-oxoacid dehydrogenase; KM