
Defect in fatty acid esterification of dolichol in Niemann-Pick type C1 mouse livers in vivo
Keywords: NPC; Niemann-Pick type C disease; ADAT; acyl-coenzyme A dolichol acyltransferase; ACAT; acyl-coenzyme A cholesterol acyltransferase; dolichyl-P; dolichyl monophosphate; CPT; cis-prenyltransferase; DEHP; diethylhexylphtalate; PFOA; perfluorooctanoic acid