
Creatine metabolism and the urea cycle
Keywords: GAA, guanidinoacetate; SAM, S-adenosylmethionine; SAH, S-adenosyl homocysteine; ROS, reactive oxygen species; AGAT, l-arginine:glycine amidinotransferase; GAMT, guanidinoacetate methyltransferase; UCD, urea cycle disorderGuanidinoacetate; Gyrate atrophy;