Keywords: سدیم فنیل بوتیرات; Urea cycle disorders; Glycerol phenylbutyrate; Children; Infants; Ammonia; Glutamine; ARG1; arginase 1; ASL; argininosuccinate lyase; ASS; argininosuccinate synthetase; BMI; body mass index; BSA; body surface area; CDC; Centers for Disease Control and Pre
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: سدیم فنیل بوتیرات; Glycerol phenylbutyrate; RAVICTI; Ammonia; Metabolic disorders; GPB; glycerol phenylbutyrate (generic name for glyceryl tri (4-phenylbutyrate), also referred to as HPN-100 or RAVICTI®); NaPBA; sodium phenylbutyrate; UCD; urea cycle disorder;
Keywords: سدیم فنیل بوتیرات; NaPBA; sodium phenylbutyrate; UCD; urea cycle disorder; BCAA; branched-chain amino acids; RDCRN; Rare Diseases Clinical Research Network; GLM; generalized linear model; OTCD; ornithine transcarbamylase deficiency; BCKDK; branched-chain ketoacid dehydrogen
Keywords: سدیم فنیل بوتیرات; ASL; argininosuccinate lyase; ASS; argininosuccinate synthase; AUC0-24; 24Â hour area under the curve; GPB; glycerol phenylbutyrate (generic name for glyceryl tri (4-phenylbutyrate), also referred to as HPN-100 or RAVICTI®); NaPBA; sodium phenylbutyrat
Targeting the enhanced ER stress response in Marinesco-Sjögren syndrome
Keywords: سدیم فنیل بوتیرات; Marinesco-Sjögren syndrome; ER stress; Lymphoblastoid cell line; Tunicamycin; Apoptosis; Tauroursodeoxycholic acid; 4-PBA; sodium phenylbutyrate; ATF6α; activating transcription factor 6α; CASP3; caspase-3; DEXA; dexamethasone; EBV; Epstein-Barr virus;
Sodium phenylbutyrate abrogates African swine fever virus replication by disrupting the virus-induced hypoacetylation status of histone H3K9/K14
Keywords: سدیم فنیل بوتیرات; African swine fever virus; Histone deacetylases enzymes; Histone deacetylases inhibitors; Sodium phenylbutyrate; Enrofloxacin; Antivirals;
9-Norbornyl-6-chloropurine (NCP) induces cell death through GSH depletion-associated ER stress and mitochondrial dysfunction
Keywords: سدیم فنیل بوتیرات; NCP; 9-norbornyl-6-chloropurine; GST; glutathione-S-transferase; GSH; L-glutathione reduced; MMP; mitochondrial membrane potential; GR; glutathione reductase; PI; propidium iodide; 4-PBA; sodium phenylbutyrate; QUER; quercetin; ALLO; allopurinol; ABT; 1-a
Sodium phenylbutyrate reverses lysosomal dysfunction and decreases amyloid-β42 in an in vitro-model of inclusion-body myositis
Keywords: سدیم فنیل بوتیرات; Aβ42; amyloid beta 42; AD; Alzheimer disease; Baf; bafilomycin A1; CHMFs; cultured human muscle fibers; Chl; chloroquine; HDAC; histone deacetylase; iNOS; inducible nitric oxide synthase; NaPB; sodium phenylbutyrate; PD; Parkinson disease; s-IBM; sporadi
Elevated phenylacetic acid levels do not correlate with adverse events in patients with urea cycle disorders or hepatic encephalopathy and can be predicted based on the plasma PAA to PAGN ratio
Keywords: سدیم فنیل بوتیرات; GEE; generalized estimating equations; GPB; glycerol phenylbutyrate (generic name for glyceryl tri (4-phenylbutyrate), also referred to as HPN-100 or RAVICTI®); HE; hepatic encephalopathy; NaPBA; sodium phenylbutyrate (BUPHENYL®); PAA; phenylacetic acid
Ammonia Control in Children Ages 2 Months through 5 Years with Urea Cycle Disorders: Comparison of Sodium Phenylbutyrate and Glycerol Phenylbutyrate
Keywords: سدیم فنیل بوتیرات; ASA; Argininosuccinic acid; ASL; Argininosuccinate lyase; ASS; Argininosuccinate synthetase; AUC0-24; 24-hour area under the curve; DSMB; Data and safety monitoring board; G tube; Gastrostomy tube; GPB; Glycerol phenylbutyrate; NaPBA; Sodium phenylbutyrat
Urinary phenylacetylglutamine as dosing biomarker for patients with urea cycle disorders
Keywords: سدیم فنیل بوتیرات; ASL; argininosuccinate lyase deficiency; ASS; argininosuccinate synthetase deficiency; AUC0-24; 24Â hour area under the curve; CV%; coefficient of variation; DSMB; Data Safety and Monitoring Board; GPB; glycerol phenylbutyrate (generic name for glyceryl
New insights in nutritional management and amino acid supplementation in urea cycle disorders
Keywords: سدیم فنیل بوتیرات; Branched chain amino acids; Sodium phenylbutyrate; Urea cycle disorders
Identification of phenylbutyrate-generated metabolites in Huntington disease patients using parallel liquid chromatography/electrochemical array/mass spectrometry and off-line tandem mass spectrometry
Keywords: سدیم فنیل بوتیرات; Sodium phenylbutyrate; Huntington disease; LCECA; Metabolites; Parallel LC/EC array/MS; Tandem mass spectrometry