دانلود مقالات ISI درباره نوع Ataxia spinocerebellar 1 + ترجمه فارسی

Mitochondrial impairments contribute to Spinocerebellar ataxia type 1 progression and can be ameliorated by the mitochondria-targeted antioxidant MitoQ

Keywords: نوع Ataxia spinocerebellar 1; Spinocerebellar ataxia type 1; Purkinje cells; Mitochondria; Oxidative stress; Electron transport chain (ETC) activities; Neurodegeneration; Antioxidant MitoQ;

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2016 سفارش ترجمه

SCA1 patients may present as hereditary spastic paraplegia and must be included in spastic-ataxias group

Keywords: نوع Ataxia spinocerebellar 1; SCA; Spinocerebellar ataxia type 1; SCA1; Pyramidal signs; Spasticity;

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2015 سفارش ترجمه

Long-term oral administration of the NMDA receptor antagonist memantine extends life span in spinocerebellar ataxia type 1 knock-in mice

Keywords: نوع Ataxia spinocerebellar 1; Spinocerebellar ataxia type 1; NMDA receptor; Memantine; Purkinje cells; Dorsal motor nucleus of vagus; Neurodegenerative disease;

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2015 سفارش ترجمه

Age-, tissue- and length-dependent bidirectional somatic CAG•CTG repeat instability in an allelic series of R6/2 Huntington disease mice

Keywords: نوع Ataxia spinocerebellar 1; HD; Huntington disease; DM; myotonic dystrophy; DM1; myotonic dystrophy type 1; PCR; polymerase chain reaction; YAC; yeast artificial chromosome; BAC; bacterial artificial chromosome; SP-PCR; small pool-PCR; SCA1; spinocerebellar ataxia type 1; SCA7; spin

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2015 سفارش ترجمه

Selective multifaceted E3 ubiquitin ligases barricade extreme defense: Potential therapeutic targets for neurodegeneration and ageing

Keywords: نوع Ataxia spinocerebellar 1; AAD; active adenylation domain; 4-PBA; 4-phenylbutyric acid; 6-OHDA; 6-hydroxydopamine; ABCG5/8; ATP-binding cassette sub-family G member 5/8; AD; Alzheimer's disease; AIB1; amplified in breast cancer 1; AIP4; atrophin-1 interacting protein 4; AMPA; α-

دانلود رایگان متن کامل مقاله ISI 54 صفحه سال انتشار : 2015 سفارش ترجمه

RNAi or overexpression: Alternative therapies for Spinocerebellar Ataxia Type 1

Keywords: نوع Ataxia spinocerebellar 1; Spinocerebellar Ataxia Type 1; Ataxin-1; Ataxin-1-like; miRNA; RNAi; AAV; Cerebellum; Neurodegeneration; Polyglutamine

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2013 سفارش ترجمه

Toxic effects of expanded ataxin-1 involve mechanical instability of the nuclear membrane

Keywords: نوع Ataxia spinocerebellar 1; SCA1; spinocerebellar ataxia type 1; ATXN1; ataxin 1; polyglutamine; polyQ; SBMA; spinal bulbar muscular atrophy; HD; Huntington disease; DRPLA; dentatorubropallidoluysian atrophy; NLS; nuclear localization signal; RBM17; RNA-binding motif protein 17; AFM

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2012 سفارش ترجمه

The neurochemical profile quantified by in vivo 1H NMR spectroscopy

Keywords: نوع Ataxia spinocerebellar 1; AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; BOLD; blood-oxygen-level dependence; CNS; central nervous system; CSI; chemical shift imaging; CRLB; Cramér-Rao lower bound; fMRI; functional MRI; GABA; γ-aminobutyrate; Glx; glutamate plus gl

دانلود رایگان متن کامل مقاله ISI 21 صفحه سال انتشار : 2012 سفارش ترجمه

Neurodegeneration, Neuroprotection, and Disease-Oriented NeuroscienceResearch PaperThe design and delivery of a thermally responsive peptide to inhibit S100B-mediated neurodegeneration

Keywords: نوع Ataxia spinocerebellar 1; S100B; spinocerebellar ataxia type 1; cerebellum; neurodegeneration; elastin-like polypeptide; thermal targeting; ELP; elastin-like polypeptide; FBS; fetal bovine serum; GFP; green fluorescent protein; SCA1; spinocerebellar ataxia type 1; PC; Purkinje cel

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2011 سفارش ترجمه

Molecular actions and therapeutic potential of lithium in preclinical and clinical studies of CNS disorders

Keywords: نوع Ataxia spinocerebellar 1; Apoptosis; Brain-derived neurotrophic factor (BDNF); Glycogen synthase kinase 3 (GSK-3); Lithium; Neurodegenerative diseases; Neuroprotection; 3-NP; 3-nitropropionic acid; Aβ; β-amyloid; AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; AP-1;

دانلود رایگان متن کامل مقاله ISI 24 صفحه سال انتشار : 2010 سفارش ترجمه

Brain white matter damage in SCA1 and SCA2. An in vivo study using voxel-based morphometry, histogram analysis of mean diffusivity and tract-based spatial statistics

Keywords: نوع Ataxia spinocerebellar 1; Voxel-based morphometry; Tract-based spatial statistics-MR imaging; Ataxia; Spinocerebellar ataxia type 1; Spinocerebellar ataxia type 2; Olivopontocerebellar atrophy

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2008 سفارش ترجمه

Intranuclear immunolocalization of 14-3-3 protein isoforms in brains with spinocerebellar ataxia type 1

Keywords: نوع Ataxia spinocerebellar 1; 14-3-3 proteins; Spinocerebellar ataxia type 1; Ataxin 1; Neuronal intranuclear inclusion; Polyglutamine disease

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2007 سفارش ترجمه