Wiskott-Aldrich Syndrome: Immunodeficiency resulting from defective cell migration and impaired immunostimulatory activation
Keywords: خوشه فعال سازی بیش از حد مولکولی; WAS; Wiskott-Aldrich Syndrome; WASp; WAS protein; DC; dendritic cell; XLT; X-linked neutropenia; WAS KO; WASp knockout; VCA; verprolin homology, central and acidic; GBD; GTPase binding domain; TCR; T cell receptor; IS; immunological synapse; SMAC; supra