Oxidative stress in Niemann-Pick type C patients: a protective role of N-butyl-deoxynojirimycin therapy
Keywords: NPC, Niemann-Pick type C; ROS, reactive oxygen species; TBA-RS, thiobarbituric acid-reactive species; TAS, total antioxidant status; GSH-Px, glutathione peroxidase (GSH-Px); GSH, glutathione; SOD, superoxide dismutase; CAT, catalaseNiemann-Pick type C; Ly