
Thapsigargin and flavin adenine dinucleotide ex vivo treatment rescues trafficking-defective gp91phox in chronic granulomatous disease leukocytes
Keywords: CGD, chronic granulomatous disease; EBV, Epstein–Barr virus; Endo-H, endoglycosidase H; ER, endoplasmic reticulum; FAD, flavin adenine dinucleotide; H338Y, amino acid change of His-338 to Tyr; THAPS, thapsigargin; NADPH oxidase, nicotinamide adenine dinuc