
Keywords: autophagy; FEV1; lymphangioleiomyomatosis; sirolimus; VEGF-D; 6-MWD; 6-min walk distance; AML; angiomyolipoma; Dlco; diffusion coefficient for carbon monoxide; DLT; dose-limiting toxicity; LAM; lymphangioleiomyomatosis; MTD; maximal tolerated dose; NCI; N