Keywords: بیماری فون ویلبراند; BAT; PBQ; Katsanis epistaxis scoring system; von Willebrand disease; platelet function disorder; Ag; Antigen; BAT; Bleeding assessment tool; ESS; Epistaxis scoring system; ISTH; International Society on Thrombosis and Haemostasis; PBQ; Pediatric Bleeding
مقالات ISI بیماری فون ویلبراند (ترجمه نشده)
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Keywords: بیماری فون ویلبراند; von Willebrand disease; von Willebrand factor; Mucocutaneous bleeding;
Keywords: بیماری فون ویلبراند; von Willebrand disease; Hepatectomy; Activated partial thromboplastin time;
Keywords: بیماری فون ویلبراند; Hematologic pregnancy complication; Postpartum hemorrhage; von Willebrand disease; Hemophilia; Blood coagulation factor deficiencies; Fibrinogen deficiency; Bernard-Soulier syndrome; Glanzmann thrombasthenia; Pregnancy;
Keywords: بیماری فون ویلبراند; Cd; cadmium; vWF; von Willebrand factor; ERG; ETS-related gene; NF-κB; nuclear factor kappa B; siRNA; small interfering RNA; ECs; endothelial cells; VWD; von Willebrand disease; HUVECs; human umbilical vein endothelial cells; FBS; fetal bovine serum; PBS
Keywords: بیماری فون ویلبراند; IPDs; inherited platelet disorders; PBQ; Pediatric Bleeding Questionnaire; VWD; von Willebrand disease; RBC; red blood cells; ISTH-BAT; International Society on Thrombosis and Haemostasis Bleeding Assessment Tool; Inherited platelet disorders; Inherited t
Keywords: بیماری فون ویلبراند; haemophilia; von Willebrand disease; dental extraction; factor replacement; desmopressin;
Keywords: بیماری فون ویلبراند; Genotyping; Bleeding disorder; Hemophilia; von Willebrand disease;
Keywords: بیماری فون ویلبراند; VWF; von Willebrand factor; VWD; von Willebrand disease; DDAVP; 1-desamino-8-D-arginine vasopressin; SPR; surface plasmon resonance; HXMS; hydrogen-deuterium exchange mass spectrometry; LRR; leucine-rich repeat; VWF:Ag; VWF antigen; VWF:RCo; VWF ristoce
Keywords: بیماری فون ویلبراند; bleeding disorder; postpartum hemorrhage; pregnancy; von Willebrand disease;
Keywords: بیماری فون ویلبراند; AUC; area under the curve; BAT; bleeding assessment tool; BS; bleeding score; BSS; bleeding score system; CI; 95% confidence intervals; CNS; central nervous system; EN-RBD; European Network of Rare Bleeding Disorders; F; factor; RBD; rare bleeding disorde
Keywords: بیماری فون ویلبراند; CLA; Chemiluminescent assay; ELISA; enzyme linked immunosorbent assay; FVIII:C; FVIII coagulant; GPIb; glycoprotein Ib; HMW; high molecular weight (VWF); LIA; latex-particle immuno-assay; VWD; von Willebrand disease; VWF; von Willebrand factor; VWF Ac; VW
Keywords: بیماری فون ویلبراند; Bleeding disorders; Coagulation; von Willebrand disease; Hemophilia; Platelet defects;
Keywords: بیماری فون ویلبراند; von Willebrand disease; VWD; diagnosis; von Willebrand factor; VWF; laboratory testingADAMTS-13, a disintegrin and metalloproteinase with a thrombospondin type 1 motif, member 13; CB/Ag, collagen binding to antigen ratio; CLIA, chemiluminescent immunoassa
Keywords: بیماری فون ویلبراند; Desmopressin; Haematological disorders; Surgical bleeding; Haemophilia; von Willebrand disease
Keywords: بیماری فون ویلبراند; AVWS; acquired von Willebrand syndrome; ELISA; enzyme linked immunosorbent assay; EQA; external quality assessment; FVIII:C; FVIII coagulant; GPIb; glycoprotein Ib; HMW; high molecular weight (VWF); LIA; latex-immuno-assay; VWD; von Willebrand disease; VW
Keywords: بیماری فون ویلبراند; Facteur von Willebrand; maladie de Willebrand; Von Willebrand factor; von Willebrand disease;
Keywords: بیماری فون ویلبراند; AT; antithrombin; AZ; AstraZeneca; CAT; calibrated automated thrombogram; ETP; endogenous thrombin potential; LT; lag time; HTS; high-throughput screening; PPP; platelet poor plasma; PRP; platelet rich plasma; RU; resonance units; SPR; surface plasmon res
Keywords: بیماری فون ویلبراند; von Willebrand disease; Bleeding disorder; Dental management
Keywords: بیماری فون ویلبراند; Von Willebrand disease; hematology; pediatrics; menorrhagia; bleeding assessment
Keywords: بیماری فون ویلبراند; Paediatric bleeding; Coagulopathy; Von Willebrand disease; Coagulation testsSangrado infantil; Coagulopatía; Enfermedad de von Willebrand; Pruebas de coagulación
Risques en dermatologie interventionnelle chez les patients hémophiles ou atteints de la maladie de Willebrand
Keywords: بیماری فون ویلبراند; Hémophilie A; Hémophilie B; Maladie de Willebrand; Chirurgie dermatologique; Risque hémorragique; Hemophilia A; Hemophilia B; Von Willebrand disease; Dermatologic surgery; Bleeding complications;
Genetics of Hypercoagulable and Hypocoagulable States
Keywords: بیماری فون ویلبراند; Factor V Leiden; Prothrombin gene mutation; Protein C and S deficiencies; Antithrombin deficiency; Antiphospholipid syndrome; von Willebrand disease; Hemophilia;
Differential sensitivity of von Willebrand factor activity assays to reduced VWF molecular weight forms: A large international cross-laboratory study
Keywords: بیماری فون ویلبراند; ELISA; enzyme linked immunosorbent assay; GPIb; glycoprotein Ib; HMW; high molecular weight (VWF); NAC; Nâacetycysteine; TTP; thrombotic thrombocytopenic purpura; VWF; von Willebrand factor; VWF:Ab; VWF activity assays based on the binding of a monoclon
Haemate P â zastosowanie w profilaktyce i leczeniu krwawieÅ w chorobie von Willebranda oraz indukcji immunotolerancji w hemofilii A powikÅanej inhibitorem
Keywords: بیماری فون ویلبراند; Haemate P; choroba von Willebranda; hemofilia A; indukcja tolerancji immunologicznej; Haemate P; von Willebrand disease; Haemophilia A; Immune tolerance induction;
Full Length ArticleFeasibility of the Von Willebrand disease PREVENT trial
Keywords: بیماری فون ویلبراند; Menorrhagia; Von Willebrand disease; Von Willebrand factor; Women's health;
Hématome sous-dural aigu spontané : rechercher la maladie de Willebrand
Keywords: بیماری فون ویلبراند; Hématome sous-dural aigu spontané; Atraumatique; Céphalée; Maladie de Willebrand; Coagulopathie; Hémostase; Acute spontaneous subdural hematoma; Non traumatic; Headache; Von Willebrand disease; Coagulopathy; Hemostasis;
Review ArticleVon Willebrand disease mutation spectrum and associated mutation mechanisms
Keywords: بیماری فون ویلبراند; Von Willebrand disease; Von Willebrand factor; Hemostasis; Mutation spectrum; Mutation mechanism;
The Von Willebrand Factor A1-Collagen III Interaction Is Independent of Conformation and Type 2 Von Willebrand Disease Phenotype
Keywords: بیماری فون ویلبراند; SPR; surface plasmon resonance; CD; circular dichroism; VWF; von Willebrand factor; ULVWF; unusually large von Willebrand factor; VWD; von Willebrand disease; DDAVP; 1-desamino-8-d-arginine vasopressin; RCAM; reduced and carboxyamidated; collagen; GPIbα;
Chromosome Xq13.2 Microduplication Involving an X-Inactivation Gene in a Girl with Short Stature, Madelung Deformity, and von Willebrand Disease
Keywords: بیماری فون ویلبراند; Menorrhagia; Short stature; X chromosome aberrations; Madelung deformity; Pulmonic stenosis; XIST gene; Turner syndrome; von Willebrand disease; Connective tissue dysplasia;
Revisión de los pacientes estudiados por coagulopatÃa en una unidad de OncohematologÃa
Keywords: بیماری فون ویلبراند; Sangrado infantil; CoagulopatÃa; Enfermedad de von Willebrand; Pruebas de coagulación; Pediatric bleeding; Coagulopathy; Von Willebrand disease; Coagulation tests;
Perioperative Approach to Anticoagulants and Hematologic Disorders
Keywords: بیماری فون ویلبراند; Preoperative evaluation; Coagulopathy; Coagulation disorder; Hemophilia; Von Willebrand disease; Thrombocytopenia; Immune thrombocytopenia; Drug-induced thrombocytopenia;
Clinical use of Haemate® P in von Willebrand disease: A 25-year retrospective observational study
Keywords: بیماری فون ویلبراند; Haemate; Humate; von Willebrand disease; Haemophilia A; von Willebrand factor; Factor VIII;
ADAMTS13 content and VWF multimer and triplet structure in commercially available VWF/FVIII concentrates
Keywords: بیماری فون ویلبراند; Wilate®; ADAMTS13; VWF triplets; von Willebrand factor; VWF/FVIII concentrate; ADAMTS13; A Disintegrin And Metalloproteinase with a ThromboSpondin type 1 motif, member 13; Act; activity; Ag; antigen; BW; body weight; FRET; fluorescence resonance energy t
Von Willebrand Disease: diagnosis and management
Keywords: بیماری فون ویلبراند; bleeding assessment tools; haemostasis; mucocutaneous haemorrhage; purpura; Von Willebrand Disease; Von Willebrand factor
The co-influence of VWD type 2B/2M mutations in the A1 domain and platelet GPIbα on the rate of cleavage to VWF by ADAMTS13
Keywords: بیماری فون ویلبراند; ADAMTS13; a disintegrin and metalloprotease with thrombospondin type 1 repeats, member 13; VWF; von Willebrand factor; VWD; von Willebrand disease; RIPA; ristocetin-induced platelet aggregation; BSA; bovine serum albumin; FRETS-VWF73; fluorescence reson
von Willebrand disease, molecular biology and diagnosis
Keywords: بیماری فون ویلبراند; von Willebrand disease; Von Willebrand factorEnfermedad de von Willebrand; Factor de von Willebrand
Comparison of Von Willebrand factor (VWF) activity VWF:Ac with VWF ristocetin cofactor activity VWF:RCo
Keywords: بیماری فون ویلبراند; AVWS; acquired Von Willebrand syndrome; BCS; Behring Coagulation System; FVIII:C; coagulation factor VIII; GPIb; platelet receptor glycoprotein Ib; HMW; high molecular weight; U/ml; units per milliliter; VWD; Von Willebrand disease; VWF; Von Willebrand fa
Keywords: بیماری فون ویلبراند; Von Willebrand factor; vWf:Ag; vWf:CBA; Exercise; Von Willebrand disease
Treating symptomatic coronary artery disease in patients with Von Willebrand disease
Keywords: بیماری فون ویلبراند; Von Willebrand disease; Coronary artery disease; Acute coronary syndrome
Prevalence of Hemostatic Disorders in Adolescents with Abnormal Uterine Bleeding
Keywords: بیماری فون ویلبراند; Abnormal uterine bleeding; Hemostatic disorders; von Willebrand disease; Platelet function disorders; Adolescents
Surgeon and haematologist: A review of comprehensive care for patients with inherited bleeding disorders in Northern Ireland
Keywords: بیماری فون ویلبراند; Inherited bleeding disorders; Haemophilia; Von Willebrand disease; Comprehensive care centre; SurgeryCCC, comprehensive care centre; UK, United Kingdom; NI, Northern Ireland; BHSCT, Belfast health and social care trust; NSAIDs, non-steroidal anti-inflamma
Inherited Abnormalities of Coagulation
Keywords: بیماری فون ویلبراند; Hemostasis; Hemophilia; von Willebrand disease; Rare factor deficiency;
Two cases of peritonsillar abscess complicated by von Willebrand disease
Keywords: بیماری فون ویلبراند; Peritonsillar abscess; Tonsillectomy; von Willebrand disease;
Management of children with inherited mild bleeding disorders undergoing adenotonsillar procedures
Keywords: بیماری فون ویلبراند; Adenoidectomy; Tonsillectomy; Mild bleeding disorders; von Willebrand disease; Platelet function disorders; Factor VII deficiency; Surgical hemorrhage; Children
Underdiagnosed Menorrhagia in Adolescents is Associated with Underdiagnosed Anemia
Keywords: بیماری فون ویلبراند; FVIII:C; Factor VIII; HSC; Hospital for Sick Children; PBAC; Pictorial blood loss assessment chart; PBQ; Pediatric Bleeding Questionnaire; PT; Prothrombin time; PTT; Partial thromboplastin time; QoL; Quality of life; VWD; von Willebrand disease; VWF:Ag; v
Nonsense mediated decay of VWF mRNA subsequent to c.7674-7675insC mutation in type3 VWD patients
Keywords: بیماری فون ویلبراند; Von Willebrand disease; Nonsense mediated mRNA decay; Premature termination codon; Von Willebrand factor
Evaluation of bleeding disorders in women with menorrhagia: a survey of obstetrician-gynecologists
Keywords: بیماری فون ویلبراند; bleeding disorder; menorrhagia; physician survey; practice patterns; von Willebrand disease;
Predictors of bleeding disorders in children with epistaxis: Value of preoperative tests and clinical screening
Keywords: بیماری فون ویلبراند; Epistaxis; Bleeding disorders; Von Willebrand disease
Inherited Disorders of Hemostasis in Dogs and Cats
Keywords: بیماری فون ویلبراند; coagulation; hemostasis; hemophilia; von Willebrand disease