Keywords: Hematopoietic stem cell transplantation; gammaretroviral vector; lentiviral vector; gene editing; site-specific endonuclease; zinc finger nuclease; CRISPR/Cas9; ADA-SCID; Adenosine deaminase-deficient severe combined immunodeficiency; CGD; Chronic granu
مقالات ISI (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: Immunology; primary immunodeficiency; whole-exome sequencing; hematopoietic stem cell transplantation; common variable immunodeficiency; severe combined immunodeficiency; hyper-IgE syndrome; AIP1; Actin-interacting protein 1; APDS; Activated PI3Kδ syndro
Clinical and molecular features of X-linked hyper IgM syndrome - An experience from North India
Keywords: X-linked hyper-IgM syndrome; CD40 ligand; Immunoglobulin class switching; Neutropenia; Mycobacterium sp.; Pulmonary alveolar proteinosis; XLHIGM; X-linked hyper IgM syndrome; IVIg; Intravenous immunoglobulin; EDTA; Ethylene diamine tetraacetate; G-CSF; Gr
Long-term outcomes of 176 patients with X-linked hyper-IgM syndrome treated with or without hematopoietic cell transplantation
Keywords: X-linked hyper-IgM syndrome; CD40 ligand; hematopoietic cell transplantation; defects in class-switch recombination; long-term outcomes; primary immunodeficiency; Karnofsky/Lansky scores; CD40LG; CD40 ligand; GVHD; Graft-versus-host disease; HCT; Hematopo
Antibiotic Prophylaxis in Primary Immune Deficiency Disorders
Keywords: Primary immune deficiency diseases; Immunodeficiency; Antibody deficiency syndromes; Antibiotic prophylaxis; AAAAI; American Academy of Allergy, Asthma, and Immunology; AOM; Acute otitis media; BAT; Bronchiectasis and Long-term Azithromycin Treatment; CF;
The X chromosome and immune associated genes
Keywords: Sex chromosomes; Genetic factors; Autoimmunity; Female preponderance; Etiopathogenesis; AID; autoimmune diseases; GWAS; genome-wide association study; PBC; primary biliary cirrhosis; MHC; major histocompatibility complex; PID; primary immunodeficiency syn
Dendritic cells from X-linked hyper-IgM patients present impaired responses to Candida albicans and Paracoccidioides brasiliensis
Keywords: CD40 ligand deficiency; fungal infections; dendritic cells; X-linked hyper-IgM syndrome; primary immunodeficiencyAPCs, Antigen-presenting cells; CD40L, CD40 ligand; DCs, Dendritic cells; iDCs, Immature DCs; mDCs, Mature DCs; PTX3, Pentraxin 3; sCD40L, Sol
CD40 agonist antibody mediated improvement of chronic Cryptosporidium infection in patients with X-linked hyper IgM syndrome
Keywords: X-linked hyper-IgM syndrome; CD40 ligand; CP-870,893; CD40-R internalization;
Toll-like receptor 7-induced naive human B-cell differentiation and immunoglobulin production
Keywords: TLR-7; resiquimod; naive human B cells; immunoglobulin class-switch recombination; X-linked hyper-IgM syndrome; AID; Activation-induced cytidine deaminase; APC; Allophycocyanin; BAFF; B cell-activating factor of TNF family; BCR; B-cell receptor; CSR; Cl