Keywords: CF; Cystic fibrosis; CGD; Chronic granulomatous disease; COPD; Chronic obstruction pulmonary disease; CRS; Chronic rhinosinusitis; CVID; Common variable immunodeficiency; PAD; Primary antibody deficiency; PIDD; Primary immunodeficiency disease; TMP-SMX; T
مقالات ISI (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: Flow cytometry; Intracellular protein; Monoclonal antibody; Primary immunodeficiency disease; Surface protein; ADA; adenosine deaminase; ALPS; autoimmune lymphoproliferative syndrome; APECED; autoimmune polyendocrinopathy-candidiasis-ectodermal dystrop
Keywords: Hematopoietic stem cell transplantation; gammaretroviral vector; lentiviral vector; gene editing; site-specific endonuclease; zinc finger nuclease; CRISPR/Cas9; ADA-SCID; Adenosine deaminase-deficient severe combined immunodeficiency; CGD; Chronic granu
Keywords: FGFs; fibroblast growth factors; WGD; whole genome duplication; JTT; Jones-Taylor-Thornton; SPR level 5; Subtree-Pruning-Regrafting - Extensive; TM; transmembrane domain; LCR; low complexity region; TS; teleost-specific; FHF; FGF homologous factor
X-Linked Agammaglobulinaemia: Outcomes in the modern era
Keywords: XLA; X-Linked Agammaglobulinaemia; Immunoglobulin; Bronchiectasis; Immune deficiency; XLA; X-Linked Agammaglobulinaemia; Btk/btk; Bruton Tyrosine Kinase; IVIG; Intravenous Immunoglobulin; SCIG; Subcutaneous Immunoglobulin; HSCT; Haematopoietic Stem Cell T
Terminal 14q32.33 deletion as a novel cause of agammaglobulinemia
Keywords: XLA; X-linked agammaglobulinemia; BTK; Bruton's tyrosine kinase; IGHC; Immunoglobulin heavy chain gene locus; SCID; Severe combined immunodeficiency syndrome; BCR; B-cell receptor; VDJ; Variable, diversity and joining gene segments; IGHM; Immunoglobulin h
Enteroviruses in X-Linked Agammaglobulinemia: Update on Epidemiology and Therapyâ
Keywords: Agammaglobulinemia; Enterovirus; Coxsackievirus B5; Polio; Pleconaril; Pocapavir; Meningoencephalitis; CEMA; chronic meningoencephalitis in agammaglobulinemia; CSF; cerebrospinal fluid; IVIG; intravenous immunoglobulin; KREC; κ-deleting recombination exc
Prevalence of BTK mutations in male Algerian patterns with agammaglobulinemia and severe B cell lymphopenia
Keywords: X linked agammaglobulinemia; XLA; BTK mutations; Algeria;
High-throughput sequencing reveals an altered T cell repertoire in X-linked agammaglobulinemia
Keywords: XLA; T cell receptor; High throughput sequencing; Junctional diversity; Amino acid sequence;
Malakoplakia and Primary Immunodeficiency
Keywords: CVID; Common variable immune deficiency; MG; Michaelis-Gutmann; SCID; Severe combined immunodeficiency; XLA; X-linked agammaglobulinemia;
Immune deficiencies, infection, and systemic immune disordersCommon variable immunodeficiency is associated with a functional deficiency of invariant natural killer T cells
Keywords: iNKT; CVID; XLA; cytokine; proliferation; α-GalCer; Alpha-galactosylceramide; CVID; Common variable immunodeficiency; FITC; Fluorescein isothiocyanate; INKT; Invariant natural killer T; PE; Phycoerythrin; SAP; Signaling lymphocytic activation molecules-a
The identification of microRNAs in the whitespotted bamboo shark (Chiloscyllium plagiosum) liver by Illumina sequencing
Keywords: C. plagiosum; Chiloscyllium plagiosum; C. milii; Callorhinchus milii; Dre; Danio rerio; Fru; Fugu rubripes; Ola; Oryzias latipes; Xla; Xenopus laevis; Xtr; Xenopus tropicalis; Hsa; Homo sapiens; Mmu; Mus musculus; miRNAs; microRNAs; PC miRNAs; putative ca
Antibiotic Prophylaxis in Primary Immune Deficiency Disorders
Keywords: Primary immune deficiency diseases; Immunodeficiency; Antibody deficiency syndromes; Antibiotic prophylaxis; AAAAI; American Academy of Allergy, Asthma, and Immunology; AOM; Acute otitis media; BAT; Bronchiectasis and Long-term Azithromycin Treatment; CF;
Diagnosis and Treatment of Gastrointestinal Disorders in Patients With Primary Immunodeficiency
Keywords: Immune System; Hypogammaglobulinemia; IBD; Inflammatory Intestinal Disease; 6-MP; mercaptopurine; AZA; azathioprine; CGD; chronic granulomatous disease; CVID; common variable immunodeficiency; FOXP3; forkhead box P3; GI; gastrointestinal; GVHD; graft-vers
Toll-like receptor 4-, 7-, and 8-activated myeloid cells from patients with X-linked agammaglobulinemia produce enhanced inflammatory cytokines
Keywords: Bruton tyrosine kinase; X-linked agammaglobulinemia; Toll-like receptors; MyD88 adapter-like protein; Toll-IL-1 receptor domain-containing adapter protein; BTK; Bruton tyrosine kinase; CVID; Common variable immunodeficiency; ERK; Extracellular signal-
Primary immunodeficiency diseases associated with increased susceptibility to viral infections and malignancies
Keywords: Immunodeficiency; viral infection; malignancies; X-linked lymphoproliferative syndrome; AR-HIES; Autosomal recessive hyper-IgE syndrome; CVID; Common variable immunodeficiency; DDR; DNA damage response; DOCK8; Dedicator of cytokinesis 8; EV; Epidermodyspl
TLR signaling and effector functions are intact in XLA neutrophils
Keywords: XLA; X-linked agammaglobulinemia; Btk; Bruton's tyrosine kinase; Ig; immunoglobulin; TLR; Toll-like receptor; LPS; lipopolysaccharide; MFI; mean fluorescence intensity; DHR; dihydrorhodamine 123; SOD; superoxide dismutase; PMA; phorbol 12-myristate 13-ace
Immune deficiencies, infection, and systemic immune disordersInfection outcomes in patients with common variable immunodeficiency disorders: Relationship to immunoglobulin therapy over 22 years
Keywords: Long-term follow up; infection outcome; complications; CVIDs; clinical phenotypes; CVID; Common variable immunodeficiency disorder; LIP; Lymphoid interstitial pneumonitis; pR2; Partial regression coefficient; XLA; X-linked agammaglobulinemia;
Potentiation of TLR9 responses for human naïve B-cell growth through RP105 signaling
Keywords: TLR; Toll-like receptor; Ig; Immunoglobulin; NF-κB; Nuclear factor kappa B; IκBα; I kappa B kinase α; CVID; common variable immunodeficiency; XLA; X-linked agammaglobulinemia; LPS; lipopolysaccharide; SP; Streptococcus pneumoniae; Naïve B cells;; Inn
Characterization of Bruton's tyrosine kinase mutations in Mexican patients with X-linked agammaglobulinemia
Keywords: Btk; XLA; Splicing; Missense; Nonsense; Insertions; Deletions
Identification of a Btk mutation in a dysgammaglobulinemic patient with reduced B cells: XLA diagnosis or not?
Keywords: XLA; Btk; Sclerosing cholangitis; Chronic obstructive pancreatitis
Differential expression and molecular characterisation of Lmo7, Myo1e, Sash1, and Mcoln2 genes in Btk-defective B-cells
Keywords: Xid; XLA; Btk; Itk; Tec; Bmx; Lmo7; Myo1e; Sash1; Mcoln2;
Common Variable Immunodeficiency: Test Indications and Interpretations
Keywords: BAFF-R; B-cell activation factor of the tumor necrosis factor family receptor; CVID; common variable immunodeficiency; ICOS; inducible costimulator; MHC; major histocompatibility complex; TACI; trans-membrane activator, calcium modulator, and cyclophilin