
Phytol-induced pathology in 2-hydroxyacyl-CoA lyase (HACL1) deficient mice. Evidence for a second non-HACL1-related lyase
Keywords: α-اکسیداسیون; 2OH-FA; 2-hydroxy fatty acid; ARD; adult Refsum disease; CNS; central nervous system; DEXA; dual energy X-ray absorptiometry; ER; endoplasmic reticulum; GC; gas chromatography; KO; knockout; LC; liquid chromatography; MEF; mouse embryonic fibroblasts; MFP